22 results
ANCA Vasculitis - GPA, MPA, Eosinophilic GPA

doi:10.1038/s41572-020-0204-y

#ANCA #Vasculitis #GPA #MPA #Eosinophilic #rheumatology #diagnosis #comparison #table
ANCA Vasculitis ... - GPA, MPA, Eosinophilic ... GPA doi:10.1038 ... #Vasculitis #GPA ... #MPA #Eosinophilic
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated ... polyangiitis (GPA ... polyangiitis (MPA ... ), and eosinophilic ... #Associated #Vasculitis
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
(C-ANCA): GPA > ... >> MPA > eGPA • ... MPO-ANCA (P-ANCA ... ): eGPA, MPA >>> ... Glomerulonephritis #Vasculitis
ANCA Associated Vasculitis (AAV) - Auto-antibodies and Differential Diagnosis

MPA → usually p-ANCA
GPA → usually c-ANCA
EGPA →
ANCA Associated ... Differential Diagnosis MPA ... GPA → usually ... c-ANCA EGPAANCA ... (MPO) C-ANCA (
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... polyangiitis (GPA ... StanfordChiefs #ANCA ... #diagnosis #algorithm
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (GPA ... Polyangiitis (MPA ... ) • Eosinophilic ... ACR2021 #Guidelines #algorithm
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (GPA ... Polyangiitis (MPA ... ) - ANCA Vasculitis ... #Polyangiitis #GPA ... #ANCA #Vasculitis
Frequency of ANCA Positivity in Different Conditions
ANCA-Associated Vasculitis
 • GPA - PR3-ANCA 75%, MPO-ANCA 20%, 5%
Different Conditions ANCA-Associated ... Vasculitis • ... GPA - PR3-ANCA 75% ... • MPA - PR3-ANCA ... • EGPA - PR3-
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: ANCA Associated ... > PR3 60% • GPA ... Hydralazine-Induced ANCA-Associated ... Vasculitis: + MPO-ANCA ... (Dx: GPA, EGPA,
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
- Anti-U1-RNP ANCA-Associated ... Vasculitis: • ... Eosinophilic granulomatosis ... Renal-limited vasculitis ... - MPO: 75-80% -