28 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Uveitis or retinal vasculitis ... pseudofolliculitis, erythema ... uveitis, retinal vasculitis ... ) • Arthritis (
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Erythema elevatum ... : • Temporal arteritis ... • Takayasu's arteritis ... : • Behcet Disease ... • Cogan syndrome
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... acneiform lesions, erythema ... like lesions, erythema ... that can confirm Behcet ... azathioprine #Behcet
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... ANCA-negative vasculitis ... IgA-associated vasculitis ... , Behcet disease ... erythematosus, Rheumatoid arthritis
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
large vessels - Arteritis ... temporalis (giant-cell arteritis ... - Takayasu arteritis ... Churg-Strauss syndrome ... - Behcet
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
GI - Felty syndrome ... Wilson's disease Pulmonary ... Spondyloarthropathies, SLE • Pulmonary ... Lyme disease, Vasculitis ... , Marfan syndrome
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Dermatomyositis Erythema ... Lyme disease Erythema ... Hypersensitivity vasculitis ... Antiphospholipid-antibody syndrome ... • Vasculitis
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
Non-Infectious Aortitis: • Vasculitides ... : Giant Cell Arteritis ... , Cogan's Syndrome ... polychondritis, Behcet's ... ANCA associated vasculitis
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... ANCA Associated Vasculitis ... , Rheumatoid Vasculitis ... , Behcet's Disease ... Kumfer @AnnKumfer #Pulmonary
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... and often causes arthritis ... , obstructive pulmonary ... : • Behçet Syndrome ... • Cogan Syndrome