513 results
Von Willebrand Disease - Clinical Presentation, Diagnosis and Management

- Dr. Eric Strong @DrEricStrong - Strong Medicine
Von Willebrand Disease ... Presentation, Diagnosis ... and Management ... #Diagnosis #Management ... #hematology #treatment
Diagnostic Schema for Hyperferritinemia

Pearl: Diseases associated with extreme elevations: 
1. HLH 
2. Still's disease 
3. Systemic
Diagnostic Schema ... Hyperferritinemia Pearl: Diseases ... Still's disease ... #Differential #Diagnosis ... #Hematology
Hypereosinophilia and Hypereosinophilic Syndrome

 • Secondary Hypereosinophilic Syndrome
 • Clinically Relevant HES Variants
 • When to
suspect underlying hematologic ... disorders • Diagnosis ... Syndrome #HES #Hematology ... #eosinophils #diagnosis ... #management #algorithm
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
- Differential Diagnosis ... disorders • Celiac disease ... Non malignant hematologic ... states • Non-hematologic ... #Differential #Diagnosis
Causes of Arterial and Venous Thrombosis - Differential Diagnosis Framework

STRUCTURAL:
 - PFO: paradoxical emboli
 - Popliteal
- Differential Diagnosis ... : - Behcet disease ... APLS:PLT ↓ HEMATOLOGIC ... #Differential #Diagnosis ... #clots #hematology
The coagulation cascade is shown, separated into different phases with their endogenous and pharmacological inhibitors shown.
small amounts of FXa ... FVIIa generating FXa ... complexes with FVa ... clot #PT #PTT #diagnosis ... #models #hematology
 End Stage Liver Disease (Cirrhosis) - Complications 
 • Ascites
 • Esophageal Varices
 • Hepatic
End Stage Liver Disease ... Complications #diagnosis ... #management #summary ... #hepatology
Approach to Von Willebrand disease (VWD)

By Matthew Ho, MD PhD @MatthewHoMD

#VWD #Von #Willebrand #VonWillebrand #disease #hematology
Von Willebrand disease ... VonWillebrand #disease ... #hematology #algorithm ... #diagnosis
Castleman's Disease and Associated Syndromes
HYALINE VASCULAR VARIANT
 • unicentric, HHV8-ve, children and young.
 • Hyalinized vessels
Castleman's Disease ... with Castleman's disease ... Autoimmune diseases ... #Castlemans #Disease ... #Variants #Diagnosis
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Differential Diaqnoses ... autoinflammatory diseases ... #diagnosis #management ... #treatment #rheumatology