6442 results
Diagnostic Schema for Hyperferritinemia

Pearl: Diseases associated with extreme elevations: 
1. HLH 
2. Still's disease 
3. Systemic
Diagnostic Schema ... HLH 2. ... #Differential #Diagnosis ... #Hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Clinical Features: Fever, Splenomegaly, Hepatomegaly, Lymphadenopathy, Confusion
Classic lab findings in HLH: ↑↑ ferritin, Anemia,
Lymphohistiocytosis (HLH ... IL-2 receptor Diagnostic ... Criteria): Molecular diagnosis ... Lymphohistiocytosis #diagnosis ... #hematology #criteria
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
Presentation / Diagnosis ... Diagnosis via genetic ... Infection should be diagnosed ... Lymphohistiocytosis #diagnosis ... management #treatment #hematology
Pancytopenia - Differential Diagnosis

Congenital Diseases:
• GATA2 deficiency
• Fanconi’s anemia
• Wiskott-Aldrich syndrome
• Ribosomopathy or telomeropathy

Cancer:
• Leukemia
• Lymphoma

Inflammatory
- Differential Diagnosis ... erythematosus • HLH ... #Differential #Diagnosis ... #Hematology
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
and Differential Diagnosis ... and Screen for HLH ... HLH syndrome 5. ... #Differential #Diagnosis ... #Algorithm #Hematology
Pancytopenia - Workup and Differential Diagnosis Algorithm
Consumption Disorders
 1. Autoimmune Mediated Pancytopenia
 2. Splenic Sequestration
Peripheral Destruction
and Differential Diagnosis ... and Screen for HLH ... HLH syndrome 5 ... #Differential #Diagnosis ... #Algorithm #Hematology
Conditions Associated With Hyperferritinemia 
DDx of extreme hyperferritinemia >10,000
Not just HLH - in fact, most common
10,000 Not just HLH ... - Malignancy—Hematologic ... - Secondary HLH ... (Babesia) - Diagnosis ... #differential #diagnosis
Hemophagocytic Lymphohistiocytosis (HLH) Diagnostic Criteria - 2004 vs 2009

At least three of the following: 
 -
Lymphohistiocytosis (HLH ... ) Diagnostic Criteria ... @PulmCrit #HLH ... Lymphohistiocytosis #Diagnosis ... #Criteria #Hematology
Causes of Hyperferritinemia - Differential Diagnosis
Ferritin > 1000
Ferritin is the storage form of iron. Increased hepcidin
- Differential Diagnosis ... HLH or Adult Onset ... Hematologic Malignancy ... In adults, HLH is ... #Differential #Diagnosis
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
diagnostic consideration ... Diagnostic Criteria ... - Diagnosis requires ... or a molecular diagnosis ... #Management #Hematology