24 results
Hemolytic Anemia - Differential Diagnosis Algorithm
Hereditary:
 • Peripheral blood smear + DAT + further History
 •
Hemolytic Anemia ... Diagnosis Algorithm Hereditary ... → Sickle Cell anemia ... → Hereditary spherocytosis ... anemia (TTP, HUS
Red Blood Cell (RBC) Morphology Atlas
 • Microcytic - Iron-deficiency anemia, Thalassemia, Sideroblastic anemia, Lead poisoning
Spherocytes - Hereditary ... spherocytosis, Hemolytic ... Elliptocytes - Hereditary ... PD deficiency, Pulmonary ... Schistocytes - Hemolytic
Causes of Extravascular and Intravascular Hemolysis - Differential Diagnosis Algorithm
Extravascular - Spleen and RES-mediated hemolysis
 -
Intravascular Hemolysis ... and RES-mediated hemolysis ... Defects • Hereditary ... spherocytosis • Hereditary ... anemia
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 • Mechanical Trauma (Microangiopathic hemolytic anemia):
Framework for Hemolysis ... Intravascular Hemolysis ... anemia): ... defects (e.g. hereditary ... diagnosis #hematology #anemia
Red Blood Cell (RBC) Morphology
Microcytic RBC: Pyridoxine deficiency, Thalassemia, Iron deficiency anemia, Chronic disease anemia (sometimes),
Microangiopathic Hemolytic ... drugs Elliptocyte: Hereditary ... Spherocyte: Hereditary ... : Hereditary stomatocytosis ... Cold autoimmune hemolytic
Hemolytic Anemia - Differential Diagnosis Algorithm
 • Sickle cells - Consider sickle cell disease (diverse genotypes):
Hemolytic Anemia ... membrane disorder (hereditary ... spherocytosis, hereditary ... ARUPConsult @ARUPLabs #Hemolytic ... #Anemia #Differential
Differential Diagnosis for Hemolytic Anemia
Intrinsic Causes:
 • Enzyme deficiencies ex. G6PD, pyruvate kinase 
 • Hemoglobinopathies
Diagnosis for Hemolytic ... Anemia Intrinsic ... Hereditary spherocytosis ... udaygulati #Hemolytic ... #Anemia #Differential
Clinical Classification of Pulmonary Hypertension

1. Pulmonary arterial hypertension from pulmonary vasculopathy
Idiopathic pulmonary arterial hypertension
Heritable gene mutations
Classification of Pulmonary ... Pulmonary arterial ... with or without hereditary ... Schistosomiasis - Chronic hemolytic ... anemia - Persistent
Elevated Lactate Dehydrogenase (LDH) - Differential Diagnosis Framework

LDH is a cytoplasmic enzyme present in tissues throughout
: • Hemolytic ... Anemias: - Spherocytosis ... anemia, PNH, immune ... - Pernicious anemia ... Legionnaires disease • Pulmonary
Classification of Jaundice
Unconjugated hyperbilirubinemia (predominantly indirect bilirubin)
 • Increased bilirubin production (eg, hemolytic anemias, hemolytic reactions,
production (eg, hemolytic ... anemias, hemolytic ... reactions, hematoma, pulmonary ... bilirubin) • Hereditary