27 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
staining): • Low Complement ... >>> MPA > eGPA ... MPO-ANCA (P-ANCA): eGPA ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Urticarial Vasculitis ... Complex Formation - Complement ... Formation -> Vasculitis ... TerrierBen #Hypocomplementemic
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Guidelines for Treatment ... Polyangiitis (EGPA ... #Management #Treatment ... ACR2021 #Guidelines #algorithm
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
capillaritis • EGPA ... often involved • Hypocomplementemic ... Urticaria and hypocomplementemia ... , EGPA, microscopic ... against MPO • Complement
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... , small-vessel vasculitis ... Complement levels ... polyangiitis (GPA ... polyangiitis (EGPA
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
Pneumonitis • Treatment ... Granulomatous DX with Vasculitis ... : GPA, EGPA
2021 ACR/VF Guidelines for Management of Eosinophilic Granulomatosis with Polyangiitis (EGPA)

#EGPA #Eosinophilic #Granulomatosis #Polyangiitis #ACR2021 #Management
Polyangiitis (EGPA ... ) #EGPA #Eosinophilic ... #rheumatology #algorithm ... #vasculitis
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... polyangiitis (GPA ... polyangiitis (eGPA ... StanfordChiefs #ANCA #Vasculitis ... differential #diagnosis #algorithm
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Polyangiitis (EGPA ... ) - ANCA Vasculitis ... Management Algorithm ... @MithuRheum #EGPA ... #Management #Treatment
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... polyangiitis), EGPA ... DAH), asthma in EGPA ... palpable purpura 2/2 vasculitis ... diagnosis #management #treatment