18 results
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Diagnosis and Management ... of Hypocomplementemic ... Urticarial Vasculitis ... 3) Hypocomplementemia ... TerrierBen #Hypocomplementemic
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
Vasculitis A group ... , small-vessel vasculitis ... Complement levels ... polyangiitis (MPA ... vasculitis - MPO
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
myeloperoxidase (MPO-ANCA ... often involved • Hypocomplementemic ... Urticaria and hypocomplementemia ... Vasculitis: + MPO-ANCA ... • Complement
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
(C-ANCA): GPA > ... MPO-ANCA (P-ANCA ... ): eGPA, MPA >>> ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Urticarial Vasculitis ... Complex Formation - Complement ... Formation -> Vasculitis ... TerrierBen #Hypocomplementemic
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
) - ANCA Vasculitis ... Management Algorithm ... #ANCA #Vasculitis ... #Management #Treatment ... ACR2021 #Guidelines #algorithm
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
: ANCA Associated ... myeloperoxidase (MPO-ANCA ... > PR3 60/ GPA ... Elevated AST ALT • Hypocomplementemia ... ) • Hypocomplementemic
2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Guidelines for Management ... Polyangiitis (MPA ... #Polyangiitis #MPA ... #rheumatology #algorithm ... #vasculitis
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (GPA ... Polyangiitis (MPA ... @MithuRheum #Vasculitis ... ACR2021 #Guidelines #algorithm
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... polyangiitis (GPA ... StanfordChiefs #ANCA ... #diagnosis #algorithm