56 results
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
of Hypocomplementemic ... ) Diagnosis of ... HUV 1) Chronic ... vasculitis 3) Hypocomplementemia ... TerrierBen #Hypocomplementemic
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Complex Formation - Complement ... TerrierBen #Hypocomplementemic ... Urticarial #Vasculitis #HUV
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Causes of Hypocomplementemia ... @AnnKumfer #Hypocomplementemia ... #Low #Complement ... CHAMPS #Mnemonic #diagnosis ... #differential #
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
pseudotumor 4 phenotypes ... PET-CT Imaging (→ Diagnostic ... rheumatoid factor), ± hypocomplementemia ... Related #Disease #diagnosis ... #management #phenotypes
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitides - Differential ... Diagnosis Framework ... often involved • Hypocomplementemic ... Urticaria and hypocomplementemia ... against MPO • Complement
Thrombotic Microangiopathies - Primary Thrombotic Microangiopathy (TMA) - Differential Diagnosis Table

 • Thrombotic Thrombocytopenic Purpura (TTP)
Microangiopathy (TMA) - Differential ... Diagnosis Table ... - Complement-mediated ... TMA #hematology #differential ... #diagnosis #HUS
Oral Cavity Lesions in a patient with HIV/AIDS
White plaque
 - Pseudo-membranous candidiasis
 - Oral hairy leukoplakia
a patient with HIV ... candidiasis - HSV ... Mass - Wart (HPV ... Lesions #HIVAIDS #Differential ... #Diagnosis #Algorithm
Genital Ulcer - Differential Algorithm
Painful
 - H. ducreyi (Chancroid)
 - HSV
Painless
 - T pallidum (Chancre)
 -
Genital Ulcer - Differential ... Algorithm Painful ... Chancroid) - HSV ... Genital #Ulcers #Differential ... #Algorithm #Diagnosis
Causes of Extravascular and Intravascular Hemolysis - Differential Diagnosis Algorithm
Extravascular - Spleen and RES-mediated hemolysis
 -
Intravascular Hemolysis - Differential ... Diagnosis Algorithm ... perfringens - Complement-Mediated ... MAHA (TTP, DIC, HUS ... #Diagnosis #Algorithm
Differential diagnosis of schistocytes / fragmentation hemolysis:
 • Thrombotic microangiopathies (TMA)
    - TTP
Differential diagnosis ... ) - Complement-mediated ... known as atypical HUS ... #schistocytes #differential ... #diagnosis #hematology