13 results
Cutaneous and Systemic Findings in Dermatomyositis
Cutaneous Findings:
 - Heliotrope sign and edema
 - Nail-fold changes
 -
Systemic Findings in Dermatomyositis ... Photodistributed eruption - Poikiloderma ... and V-neck sign ... #Dermatomyositis ... #Diagnosis #Rheumatology
Shawl sign poikiloderma in Dermatomyositis

Poikiloderma in general is a common finding in older individuals with chronic
Shawl sign poikiloderma ... in Dermatomyositis ... along with other signs ... RashDecisionz #Shawl #sign ... Dermatology #Clinical #Photo
Holster Sign in Dermatomyositis

Interestingly, poikiloderma and violaceous erythema can occur in sun protected areas as well
Holster Sign in ... Dermatomyositis ... Interestingly, poikiloderma ... Thighs #SkinRash #Dermatomyositis ... Dermatology #Clinical #Photo
Poikiloderma of Civatte (Photodamage Poikiloderma)

Poikiloderma in general is a common finding in older individuals with chronic
Poikiloderma of ... ) Poikiloderma ... of dermatomyositis ... along with other signs ... Dermatology #Clinical #Photo
Approach to a Positive (+) Rheumatoid Factor (RF)
(+) RF does not always = RA
Rheumatic disorders:
 •
Polymyositis & Dermatomyositis ... Inflammatory disorders of Liver ... Rheumatoid #Factor #RF #rheumatology ... #differential #diagnosis
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
chest (in a V-sign ... disease and ILD • Liver ... Liver biopsies show ... #rheumatology # ... dermatology #diagnosis
Autoimmune Myositis
Necrotizing myopathy is associated with higher CK levels, greater level of muscle weakness, less systemic
Dermatomyositis ... heliotrope rash, Shaw sign ... , holster sign, ... /full triad at diagnosis ... #rheumatology
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
skin thickening Signs ... telangiectasias, poikiloderma ... Scleroderma #SSc #rheumatology ... #diagnosis #signs
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
Polymyositis / Dermatomyositis ... Anti-LKM (liver ... Associations #diseases #diagnosis ... #table #rheumatology
Inflammatory Myopathies
Dermatomyositis
 • Onset: Subacute
 • Pattern: Proximal
 • CK: Up to 50X ULN
 • Autoantibodies:
Inflammatory Myopathies Dermatomyositis ... heliotrope, shawl sign ... Associated Features: Diagnosis ... #differential #diagnosis ... #comparison #rheumatology