103 results
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• MM • WM • MGUS ... • MGCSMGRS ... Dermato-neuro syndrome) MGRS ... Fibrillar deposits: • Amyloidosis ... CVS+joints) • Amyloidosis
Monoclonal Gammopathy Testing
Strengths, Weaknesses and Accuracy Compared
 - SPEP 
 - IFE 
 - FLC
Protein #Diagnosis #MGRS ... #MGUS #SPEP #IFE
Echo Parameters for Differential Diagnosis in Cardiac Amyloidosis
GLS
GCS
GRS
EFSR
RELAPS
SAB

#Echocardiogram #Parameters #echocardiography #Cardiac #Amyloidosis #diagnosis
Diagnosis in Cardiac Amyloidosis ... GLS GCS GRS ... echocardiography #Cardiac #Amyloidosis
Therapy for AL Amyloidosis 2019 
 - Antibodies (Plasma cells) 
 - Proteasome Inhibitors 
 -
Therapy for AL Amyloidosis ... Amyloid_Planet #Amyloidosis ... #ALAmyloidosis
MGRS - Monoclonal Gammopathy of Renal Significance 

#MGRS #Monoclonal #Gammopathy #Renal #Significance #Diagnosis #Pathology
MGRS - Monoclonal ... Significance #MGRS
Amyloidosis Diagnosis
1) Patient presentation
 • Cardiac-specific signs of amyloidosis: Diastolic heart failure, Heart failure with preserved
Amyloidosis Diagnosis ... Cardiac-specific signs of amyloidosis ... Noncardiac signs of amyloidosis ... significance (MGUS ... neuropathy, atypical MGUS
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Significance (MGUS ... Renal-centered (ie "MGRS ... #Significance #MGUS
Monoclonal Gammopathy of Undetermined Significance (MGUS) - Summary Framework

Hematologic disorder characterized by the presence of either
Significance (MGUS ... IgM MGUS: • Serum ... multiple myeloma, AL amyloidosis ... Light-Chain MGUS ... myeloma and AL amyloidosis
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Amyloidosis - Summary ... Primary amyloid amyloidosis ... IBD) • Familial amyloidosis ... • Senile amyloidosis ... Amyloidosis
Multiple Myeloma and Monoclonal Gammopathies
C - HyperCalcemia- calcium > 11 mg/dL / >1 mg/dL the ULN
R
deposition disease, and amyloidosis ... diseases, CML, amyloidosis ... #Gammopathies #MGUS