21 results
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Vasculitis 1 ... 3 types 2) Vasculitis ... phenomenon • Ulcers ... Hyperviscosity syndrome ... #Rheumatology #
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... idiopathic oral ulcers ... Recurrent genital ulcers ... oral and genital ulcers ... Diagnosis #criteria #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
nodules, Deep ulcers ... Urticarial/LCV) - Cryoglobulinemic ... : • Behcet Disease ... • Cogan syndrome ... #dermatology #rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Purpura - Skin ulcers ... Hyperviscosity Syndrome ... syndrome in 80% ... (e.g. systemic lupus ... classification #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
livedo reticularis, ulcers ... : • Behçet Syndrome ... genital aphthous ulcers ... such as systemic lupus ... differential #diagnosis #rheumatology
Causes of Pharyngitis - Differential Diagnosis
Infectious:
 • Bacterial: Group A Strep, Group B and C Strep,
Viruses Autoimmune: Lupus ... , Behcet syndrome ... , ANCA vasculitis ... Autoinflammatory syndromes ... Drug-induced mucosal ulcers
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... ANCA-negative vasculitis ... , Behcet disease ... , Cryoglobulinemia ... Complex: Systemic lupus
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... recurrent oral ulcers ... following: • Genital ulcers ... Oral and genital ulcers-Topical ... signs #symptoms #rheumatology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Churg-Strauss syndrome ... - systemic lupus ... - Behcet ... - Sjögren syndrome ... Vessels #Diagnosis #Rheumatology
Mucous Membrane Disorder - Differential Diagnosis Algorithm
Erosions/Ulcers/Blisters
 - Primary Dermatologic Diseases
     •
Algorithm Erosions/Ulcers ... recurrent, punched out ulcers ... • Systemic lupus ... disease) • Behcet's ... syndrome White