13 results
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
for Treatment & ... (GPA), Microscopic ... (EGPA) Sources ... #ACR2021 #Guidelines ... #algorithm #rheumatology
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
(GPA), microscopic ... (EGPA) ... - 80-90% PR3+ ... > PR3 Dr. ... MPO #PR3 #Diagnosis
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
(GPA) and Microscopic ... ) - ANCA Vasculitis ... MPA #ANCA #Vasculitis ... #Management #Treatment ... #ACR2021 #Guidelines
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
(EGPA) - ANCA Vasculitis ... alone in select pts ... #ANCA #Vasculitis ... #Management #Treatment ... #ACR2021 #Guidelines
2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
2021 ACR/VF Guidelines ... (GPA) and Microscopic ... #GPA #Microscopic ... MPA #ACR2021 #Management ... #vasculitis
ANCA Associated Vasculitis (AAV) - Auto-antibodies and Differential Diagnosis

MPA → usually p-ANCA
GPA → usually c-ANCA
EGPA →
and Differential Diagnosis ... GPA → usually ... c-ANCA EGPAANCA ... PR3) X-ANCA (elastase ... ANCA Vasculitis
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... (GPA) • Both asthma ... (eGPA) Stanford ... #diagnosis #algorithm
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Negative IF): • PR3 ... GPA >>> MPA > eGPA ... GPA Stanford Internal ... #differential #diagnosis ... #algorithm #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
proteinase 3 (PR3 ... in >90%, MPO > PR3 ... 60% • GPA: ... 80% (80-90% have PR3 ... (Dx: GPA, EGPA,
Frequency of ANCA Positivity in Different Conditions
ANCA-Associated Vasculitis
 • GPA - PR3-ANCA 75%, MPO-ANCA 20%, 5%
GPA - PR3-ANCA 75% ... • MPA - PR3-ANCA ... • EGPA - PR3- ... - PR3-ANCA 10%, ... #MPO #PR3 #diagnosis