18 results
#POEMS syndrome
#POEMS syndrome
POEMS Syndrome

Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal protein & Skin changes

Andrew Sanchez M.D. @ASanchez_PS

#POEMS #Syndrome #diagnosis
POEMS Syndrome ... ASanchez_PS #POEMS
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Systemic Features: POEMS ... xanthogranuloma (NXG) • POEMS
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Cytokine secretion: POEMS
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#Diagnosis #Cardiology #EKG #ECG
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Achalasia Management Algorithm
 - Botulinum Injection
 - Pharmacotherapy (CCB/nitrates)
 - Pneumatic Dilation
 - Peroral Endoscopic Myotomy
Endoscopic Myotomy (POEM
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
macroglobulinosis • POEMS ... syndrome • DADS-M • POEMS ... Involvement: • POEMS
Etiologies of Peripheral Neuropathy
 • Metabolic / Nutritional: DiabetesB12 deficiency, Uremia/ESRD, Hypothyroidism
 • Medication-induced: ART, Antibiotics,
Paraprotein-associated (POEMS
Scleroderma Mimics
 • Scleredema
 • Scleromyxedema (papular mucinosis)
 • Eosinophilic Fasciitis
 • Nephrogenic Systemic Fibrosis
 •
Systemic Fibrosis • POEMS
Management of Jackhammer Esophagus or Esophageal Spasm
Step 1: Assess the severity of the motility disturbance
Step 2:
Management Step 5: POEM