67 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... ulceration • Ocular ... meningitis), MCC CNS symptoms ... inhibitors • Uveitis- Ophthalmology ... management #signs #symptoms
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and often causes arthritis ... , and ocular inflammation ... ulcers, cutaneous, ocular ... Syndrome: - Ocular ... Presentation - Systemic Symptoms
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
yrs - Cranial symptoms ... Polyarteritis nodosa: - Skin ... multiplex ANCA vasculitis ... Leukocytoclastic vasculitis ... Ulceration GI tract - Ocular
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... IgM deposits • Nodular ... : • Temporal arteritis ... • Takayasu's arteritis ... : • Behcet Disease
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... • Progressive symptoms ... , and ocular inflammation ... ulcers, cutaneous, ocular ... Cogan syndrome: Ocular
Giant Cell (Temporal) Arteritis: Pathogenesis and investigations
Risk Factors:
 - Unclear environmental triggers (may be viral, not
Cell (Temporal) Arteritis ... old; F>M Signs/Symptoms ... palpation - Vasculitic ... skin lesions ... #Vasculitis
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
infection • Lyme disease ... migrans • Lyme disease ... • Gonococcal arthritis ... Hypersensitivity vasculitis ... Antiphospholipid-antibody syndrome • Vasculitis
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
IBD, Whipple's disease ... • Whipple's disease ... - Whipple's disease ... , Vasculitis (e.g ... Scleroderma Thickened skin
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
or retinal vasculitis ... - Skin lesions ... Wide variety of skin ... , retinal vasculitis ... ) • Arthritis (
Giant Cell (Temporal) Arteritis: Clinical findings and Complications
Signs/Symptoms: 
 - Headache (usually constant, superimposed by waves
Cell (Temporal) Arteritis ... Complications Signs/Symptoms ... artery tender, nodular ... GiantCell #Temporal #Arteritis ... #diagnosis #Vasculitis