49 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
oral ulcers with 2 ... AND • Meeting ≥ 2 ... test Most Common Clinical ... #disease #Diagnosis ... #criteria #rheumatology
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Clinical triad ... Differential Diaqnoses ... • Ocular: uveitis ... #diagnosis #management ... #treatment #rheumatology
Sarcoidosis
Stage 1 - Bilateral LAD without involvement of lung parenchyma
Stage 2 - Bilateral LAD with involvement
parenchyma Stage 2 ... interstitial lung disease ... sarcoid Lofgren Syndrome ... - Triad of hilar ... #Sarcoidosis #Diagnosis
Evaluation of suspected incomplete Kawasaki Disease

1. AHA consensus recommendations
2. Infants ≤6 months old on day ≥7
incomplete Kawasaki Disease ... recommendations 2. ... if they have no clinical ... or RCA of 2–2.5 ... #Diagnosis #Peds
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... ulceration • Ocular ... : Arterial (MCC-small ... (Clinical Dx). ... signs #symptoms #rheumatology
Susac Syndrome - Clinical Triad
 - Central nervous system dysfunction
 - Branch retinal artery occlusion
 -
Susac Syndrome - ... Clinical Triad ... - Recurrent disease ... #Diagnosis #Management ... #Rheumatology
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
cases • Sjögren syndrome ... Anti-La/SSB • ... Antineutrophil #antibodies #diagnosis ... #rheumatology # ... diseases
Antiphospholipid Syndrome (APS)
APS is a rare autoimmune disorder characterized by recurring blood clots resulting from antibodies
Antiphospholipid Syndrome ... anticoagulant (LA ... at least: • 1 clinical ... presence of 1 clinical ... present Treatment (EULAR
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
(SPS) - Diagnosis ... Clinical Manifestations ... EMG testing Lab ... poisoning, Parkinson's disease ... Baclofen • Severe Disease
Rheumatic Heart Disease - Mitral Stenosis on Echocardiogram
(1) Thickened and fibrosed MV leaflets - rheumatic etiology
Rheumatic Heart Disease ... Mitral Stenosis on Echocardiogram ... (2) Lvef 25-30% ... by the LAA appears ... (7) patient in atrial