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Thrombotic Microangiopathies In Systemic Lupus Erythematosus

Dr. Laurent ARNAUD @Lupusreference

#TMAs #Thrombotic #Microangiopathies #Systemic #Lupus #Erythematosus #SLE #hematology
Microangiopathies In Systemic Lupus ... Microangiopathies #Systemic #Lupus ... #rheumatology # ... differential #diagnosis ... #causes
Faget Sign - Pulse-Temperature Dissociation
Causes of Relative Bradycardia
 • Infectious Causes: Legionella, Psittacosis, Q fever, Typhoid
Dissociation Causes ... • Infectious Causes ... Typhus, Babesiosis, Malaria ... Non-Infectious Causes ... #bradycardia #differential
Causes of Relative Bradycardia - Note the propensity for intracellular organisms.
Infectious: 
Legionella, Psittacosis, Q fever, Typhoid
Causes of Relative ... , Typhoid fever, ... Typhus, Babesiosis, Malaria ... #bradycardia #Causes ... #differential #
Causes of Fever of Unknown Origin (FUO) - Differential Diagnosis
 • Infection: Extrapulmonary tuberculosis, Abscess, Endocarditis,
Causes of Fever ... Origin (FUO) - Differential ... Lemierre's syndrome), Malaria ... . autoimmune): Lupus ... #Origin #FUO #Differential
Faget's Sign & Liebermeister's Rule
Pulse-Temperature Dissociation
EVERY 1 F RISE IN TEMPERATURE -> HR INCREASES 8-10 BPM
INFECTIOUS
BPM INFECTIOUS CAUSES ... Babesiosis • Malaria ... OTHER CAUSES ... help hone your differential ... Dissociation #diagnosis #differential
Fever Patterns - Differential Diagnosis Framework

Continuous Fever:
Temp > 38°C with only 1 degree fluctuation in 24
Differential Diagnosis ... bacteremia • Malaria ... endocarditis, malaria ... Non-Infectious Causes ... #Patterns #Differential
Systemic Lupus Erythematosus - Diagnosis
Manifestations:
 - Arthritis 69%
 - Malar rash 40%
 - Fever 36%
 -
Arthritis 69% - Malar ... rash 40% - Fever ... (aPL) 30-45% Differential ... symptoms #mimickers #differential ... #rheumatology
Causes of Fever of Unknown Origin (FUO) - Differential Diagnosis Algorithm
Neoplasm:
• NHL
• Hodgkin's lymphoma
• Leukemia
• Solid
Causes of Fever ... Origin (FUO) - Differential ... Protozoa (eg. malaria ... #FUO #Chronic #Differential ... Diagnosis #Algorithm #causes
Uveitis - Definition, Causes and SUN Classification

Inflammation of the iris, ciliary body, vitreous, retina and/or choroid
Incidence
- Definition, Causes ... retinal ischemia Causes ... Intermediate, Posterior ... Classification #Differential ... Ophthalmology #Rheumatology
Differential Diagnosis for Hemolytic Anemia
Intrinsic Causes:
 • Enzyme deficiencies ex. G6PD, pyruvate kinase 
 • Hemoglobinopathies
Differential Diagnosis ... Anemia Intrinsic Causes ... Bartonella, Babesia, Malaria ... Hemolytic #Anemia #Differential ... classification #hematology