22 results
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Systemic Sclerosis ... Scleroderma) Multi-system ... thickening Signs and Symptoms ... Raynaud's, digital ulcers ... diagnosis #signs #symptoms
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behçet's Syndrome Systemic ... thrombophlebitis, pyoderma ... like lesions, pyoderma ... meningitis), MCC CNS symptoms ... management #signs #symptoms
EULAR/ACR Classification Criteria for Systemic Lupus Erythematosus
Clinical Domains:
 • Constitutional domain: Fever
 • Cutaneous domain: Non-scarring
EULAR/ACR Classification ... Criteria for Systemic ... alopecia, Oral ulcers ... #EULARACR #Classification ... Criteria #SLE #Systemic
Systemic Lupus Erythematosus - Diagnosis
Manifestations:
 - Arthritis 69%
 - Malar rash 40%
 - Fever 36%
 -
Systemic Lupus Erythematosus ... Nephropathy 16% - Oral ulcers ... Lupusreference #SLE #Systemic ... autoantibodies #signs #symptoms
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
livedo reticularis, ulcers ... genital aphthous ulcers ... central nervous system ... Symptoms (Sx) in ... #rheumatology #classification
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
associated with systemic ... Musculoskeletal system ... Episcleritis Signs and Symptoms ... development of skin symptoms ... DDX: - Pyoderma
Traditionally, congestive heart failure has been classified according to severity of symptoms, first formulated by the
to severity of symptoms ... cardiovascular system ... III and class IV symptoms ... HeartFailure #Staging #Classification
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Symptoms (SX) in ... livedo reticularis, ulcers ... • Progressive symptoms ... purpura, nodules or ulcers ... genital aphthous ulcers
Lymphomas and Lymphoproliferative Disorders - Differential Diagnosis Algorithm
Hodgkin Lymphoma ~40% - Characteristic For Reed-Sternberg (RS) Cells
site in lymphatic system ... with lymphatic system ... pattern of spread, B symptoms ... Lymphoproliferative #Disorders #Classification
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
activate the immune system ... Purpura - Skin ulcers ... disorder (e.g. systemic ... diagnosis #types #classification