350 results
Management of Scleroderma Renal Crisis

#Scleroderma #Renal #Crisis #Management #Algorithm #Rheumatology
Management of Scleroderma ... Renal Crisis ... #Scleroderma #Renal ... #Crisis #Management
Systemic Sclerosis (Scleroderma)
Limited - CREST:
 • Calcinosis
 • Raynaud phenomenon
 • Esophageal dysmotility
 • Sclerodactyly
 •
Systemic Sclerosis (Scleroderma ... 10% - 15% • Scleroderma ... renal crisis ... Systemic #Sclerosis #Scleroderma
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Systemic Sclerosis (Scleroderma ... 3 Subtypes of Scleroderma ... distal to elbows/wrists ... Sclerosis sine scleroderma ... renal crisis (SRC
Diagnostic Criteria for Scleroderma Renal Crisis 

1. New onset blood pressure >150/85 mm Hg OR increase
Diagnostic Criteria for Scleroderma ... Renal Crisis ... shrinkage #Scleroderma ... #Renal #Crisis
Scleroderma Renal Crisis (SRC)

Clinical Presentation of Scleroderma Renal Crisis:
1) Acute kidney injury
2) Abrupt onset of hypertension
3)
Scleroderma Renal ... Crisis (SRC) ... Presentation of Scleroderma ... Renal Crisis: ... #Renal #Crisis
Differential diagnosis of schistocytes / fragmentation hemolysis:
 • Thrombotic microangiopathies (TMA)
    - TTP
hypertension • Scleroderma ... renal crisis
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Complement Levels: Scleroderma ... Renal Crisis, IgA
Scleroderma Renal Crisis - Diagnosis and management

Diaqnosis
 • De novo arterial hypertension of normotensive form +++
Scleroderma Renal ... Crisis - Diagnosis ... TerrierBen #Scleroderma
Hypertension and Altered Mental Status (AMS) - Differential Diagnosis Framework

Hypertension:
 • Hypertensive emergency
 • Hypertensive encephalopathy
Polyarteritis nodosa • Scleroderma ... renal crises
Criss-Cross Gait on Physical Exam 

Seen in Glucose Transporter type 1 Deficiency Syndrome

#CrissCross #Criss #Cross #Gait
Criss-Cross Gait ... #CrissCross #Criss ... #Cross #Gait #PhysicalExam