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Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... bullae, Ulceration, Urticaria ... - Anti-C1q (Urticarial ... : • Behcet Disease ... #dermatology #rheumatology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... - Kawasaki disease ... hypocomplementary urticarial ... Vessels #Diagnosis #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Hypocomplementemic Urticarial ... - Urticaria and ... (Granulomatous disease ... cryoglobulinemia, urticarial ... differential #diagnosis #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... gangrenosum) • Urticaria ... Granulomatous vasculitis ... • Necrotising vasculitis ... rash #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
atherosclerotic disease ... Hypocomplementemia: Urticarial ... Hypocomplementemic Urticarial ... maculopapular lesions, urticaria ... Differential #Diagnosis #Rheumatology
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... , Purpura, Urticaria ... pain (20%) Renal disease ... symptoms #diagnosis #rheumatology
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Hypocomplementemic Urticarial ... Vasculitis (HUV ... HUV 1) Chronic urticaria ... #Vasculitis #HUV ... Diagnosis #Management #Rheumatology
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Hypocomplementemic Urticarial ... Vasculitis C1q ... Hypocomplementemic #Urticarial ... #Vasculitis #HUV ... Pathophysiology #Rheumatology
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
Cold Urticaria Prevalence ... Chronic spontaneous urticaria ... Chronic inducible urticarias ... .14674 #Cold #Urticaria ... #diagnosis #rheumatology
The Associated Diseases of Cryptoglobulinemia Vasculitis
#rheumatology #causes
The Associated Diseases ... Cryptoglobulinemia Vasculitis ... #rheumatology