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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... Hypocomplementemic Urticarial ... - Urticaria and ... Presentation - Systemic Symptoms ... cryoglobulinemia, urticarial
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... • Progressive symptoms ... Hypocomplementemia: Urticarial ... Hypocomplementemic Urticarial ... maculopapular lesions, urticaria
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... , Purpura, Urticaria ... erythematosus #signs #symptoms
Vancomycin induced Leukocytoclastic Vasculitis (LCV) of the Hand
70 M vertebral osteomyelitis on vancomycin and cefepime for
Leukocytoclastic Vasculitis ... eosinophilia and systemic symptoms ... polyangiitis, HSP, urticarial ... vasculitis, ITP ... Leukocytoclastic #Vasculitis
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Hypocomplementemic Urticarial ... Vasculitis (HUV ... HUV 1) Chronic urticaria ... Leukocytoclastic vasculitis ... #Vasculitis #HUV
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... bullae, Ulceration, Urticaria ... - Anti-C1q (Urticarial
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Hypocomplementemic Urticarial ... Vasculitis C1q ... Formation -> Vasculitis ... Hypocomplementemic #Urticarial ... #Vasculitis #HUV
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
Cold Urticaria Prevalence ... and duration of symptoms ... angioedema Other symptoms ... Chronic inducible urticarias ... .14674 #Cold #Urticaria
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... ANCA-associated vasculitis ... hypocomplementary urticarial ... vasculitis
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... Cryoglobulinemic vasculitis ... syndrome • IgA vasculitis ... Small #Vessel #Vasculitides ... #vasculitis #differential