209 results
Approach to Von Willebrand disease (VWD)

By Matthew Ho, MD PhD @MatthewHoMD

#VWD #Von #Willebrand #VonWillebrand #disease #hematology
Willebrand disease (VWD ... MatthewHoMD #VWD ... VonWillebrand #disease #hematology ... #algorithm #diagnosis
Platelet disorders and Aggregometry
Glanzmann Thrombasthenia
 • Defective aggregation to all agonists except ristocetin
 • Normal platelet,
also be seen in vWD ... 1 or Type 3) — differentiate ... with qualitative defects ... Platelet #disorders #hematology ... #hemepath #differential
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... of GP Ib/IX/V [vWF ... α-granules (contains vWF ... comparison #table #differential ... #diagnosis #hematology
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
Thrombocytosis - Differential ... Diagnosis Algorithm ... Thrombocytosis #Differential ... #Diagnosis #Algorithm ... #Causes #Hematology
Hemolytic Anemias - Differential Diagnosis Algorithm

Signs of anemia and hemolysis:
 • ↓ Haptoglobin
 • ↑ LDH
Hemolytic Anemias - Differential ... Diagnosis Algorithm ... Hemolytic #Anemias #Differential ... #Diagnosis #Algorithm ... #hematology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Purpura - Differential ... PURPURA: Platelet Defects ... Willebrand disease (VWD ... Vasculopathy #Purpura #Differential ... #Diagnosis #hematology
Cardiac Murmurs and Maneuvers

An algorithm demonstrating the effect of various maneuvers on systolic murmurs. 
TR, tricuspid
Maneuvers An algorithm ... demonstrating the effect ... aortic stenosis; VSD ... ventricular septal defect ... The effect of squatting
Causes of Bleeding / Bruising - Differential Diagnosis Algorithm
Thrombocytopenia - Quantitative Defect
 • Decreased Production
 •
Bleeding / Bruising - Differential ... Diagnosis Algorithm ... - Quantitative Defect ... - Qualitative Defect ... #Causes #Hematology
Causes of Neutropenia with Pancytopenia - Differential Diagnosis Algorithm
Sequestration:
 • Splenomegaly
Marrow Infiltration:
 • Hematologic and non-hematologic
Pancytopenia - Differential ... Diagnosis Algorithm ... and non-hematologic ... #Neutropenia #Differential ... #Diagnosis #Algorithm
Approach to Thrombocytosis - Elevated Platelet Count - Differential Diagnosis Algorithm

Peripheral Smear concerning for malignancy?
Platelet Count - Differential ... Diagnosis Algorithm ... Thrombocytosis #Platelets #Differential ... #Diagnosis #Algorithm ... #hematology