48 results
Cryoglobulinemia Vasculitis
#rheumatology #diagnosis #signs
Cryoglobulinemia Vasculitis ... #rheumatology ... #diagnosis #signs
Giant Cell (Temporal) Arteritis: Pathogenesis and investigations
Risk Factors:
 - Unclear environmental triggers (may be viral, not
HLA-DR4 mutation ... yrs old; F>M Signs ... Pathophysiology #Diagnosis ... #Signs #Symptoms ... #Vasculitis
Pancytopenia - Differential Diagnosis

Congenital Diseases:
• GATA2 deficiency
• Fanconi’s anemia
• Wiskott-Aldrich syndrome
• Ribosomopathy or telomeropathy

Cancer:
• Leukemia
• Lymphoma

Inflammatory
- Differential Diagnosis ... erythematosus • HLH ... • Epstein-Barr virus ... #Differential #Diagnosis ... #Hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
Auto-amplification loop Diagnosis ... Infections+++: Virus ... Lymphohistiocytosis #diagnosis ... #management #treatment ... #summary #rheumatology
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Non-hepatitis C virus ... Cryoglobulinemia Vasculitis ... - French Vasculitis ... Cryoglobulinemia #Vasculitis ... #Management #Rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
Presentation / Diagnosis ... : HLH signs and ... Diagnosis via genetic ... #management #treatment ... #hematology
Diagnosis and management of Polyarteritis Nodosa (PAN)

Chapel Hill 2012 definition: 
Necrotizing vasculitis ofmedium or small arteries
Diagnosis and management ... Necrotizing vasculitis ... glomerulonephritis or vasculitis ... PolyarteritisNodosa #Rheumatology ... #Diagnosis #Management
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Diagnosis and Management ... (HUV) Diagnosis ... Leukocytoclastic vasculitis ... #HUV #Diagnosis ... #Management #Rheumatology
MonkeyPox Virus - Summary Review - What we know so far

 • History
 • Epidemiology
 •
MonkeyPox Virus ... Epidemiology • Signs ... • Differential Diagnosis ... • Diagnosis ... #management #virus
Causes of Thrombocytopenia - Differential Diagnosis Algorithm
 
Decreased Megakaryopoiesis
 • Aplastic Anemia
 • Toxic Damage (e.g.
- Differential Diagnosis ... Alloimmune • anti-HLA ... HUS • DIC • Vasculitis ... #Differential #Diagnosis ... Algorithm #Causes #Hematology