20 results
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Cutaneous Manifestations ... of Monoclonal Gammopathy ... Cold agglutinin disease ... manifestations #dermatology ... #skin #clinical
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Dermatological semiology of Cutaneous ... the context of cutaneous ... Connective tissue disease ... #dermatology #semiology ... lesions #diagnosis #clinical
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
resulting in a vasculitis ... Goldberg, M.D. - UCSD ... Catalog of Clinical ... Images #Clinical ... #Photo #Dermatology
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
of Clinical Significance ... nemaline myopathy Cutaneous-centered ... Ig deposition disease ... #Gammopathy #Clinical ... Differential #Diagnosis #hematology
Cutaneous manifestations associated with myelodysplastic syndrome
 • Myeloid hemopathy with the most frequent skin lesions (20%)
Cutaneous manifestations ... appearing during the disease ... leukocytoclastic vasculitis ... differential #diagnosis #dermatology ... #oncology #clinical
Cold Agglutinin Disease

3 Types of Cold Sensitive Antibodies:
  1. Cold Agglutinins (CAD)
  2. Donath-Landsteiner
Cryoglobulins (Vasculitic ... - Idiopathic monoclonal ... Viral Infection Clinical ... presentation) • Cutaneous ... hemolytic #anemia #hematology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... gangrenosum • Cutaneous ... Autoimmunity: • -MM/WM: Vasculitis ... Sneddon-Wilkinson disease ... Paraproteinemias #Hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... ) • Cutaneous Lesions ... oral ulcers in 12 ... Arthritis, AS Treatment ... : monoclonal TNF-aIpha
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Syndrome: • Clinical ... • Autoimmune diseases ... Cryoglobulins: - Single monoclonal ... - Composed of monoclonal ... Henoch-Schönlein purpura) • Cutaneous
Cutaneous larva migrans skin Rash
25 F recent Caribbean vacation, walked barefoot on sand and now with
Diagnosis is clinical ... No treatment is ... one-time dose of 12 ... migrans #skinRash #dermatology ... #clinical #photo