16 results
Cutaneous manifestations associated with myelodysplastic syndrome
 • Myeloid hemopathy with the most frequent skin lesions (20%)
Cutaneous manifestations ... myelodysplastic syndrome ... manifestations (dermatomyositis ... Calmettes #Cutaneous ... differential #diagnosis #dermatology
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Cutaneous Manifestations ... Systemic amyloidosis, Nodular ... , Syndrome Schnitzler ... monoclonal #gammopathy #Cutaneous ... manifestations #dermatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Primary: 50% Cutaneous ... IgM deposits • Nodular ... Disease • Cogan syndrome ... Vasculitis #skin #dermatology ... #rheumatology #
ANTI-MDA5 DERMATOMYOSITIS

Cutaneous manifestations:
• Periorbital heliotrope (blue-purple) rash with edema
• Erythematous rash on the face, or the
ANTI-MDA5 DERMATOMYOSITIS ... Cutaneous manifestations ... the face, or the anterior ... #rheumatology # ... dermatology #diagnosis
Facial Swelling - Differential Diagnosis Framework for Facial Edema

Infectious:
	• Dental abscess
	• Ludwig's angina
	• Vincent's angina
	• Cellulitis
	•
Autoimmune: • SLE • Dermatomyositis ... • Sjogren's syndrome ... Preeclampsia Dermatologic ... Trauma: • Ocular ... head and neck • Cutaneous
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
Sweet Syndrome ... Most common extra cutaneous ... , breast CA - Hematologic ... multiforme - Dermatomyositis ... #diagnosis #dermatology
2019 EULAR recommendations for thrombosis in (Antiphospholipid Syndrome) APS
Venous Thrombosis - Arterial Thrombosis
INR Target
Duration
Recurrence

Dr. Laurent ARNAUD
2019 EULAR recommendations ... Antiphospholipid Syndrome ... Antiphospholipid #Syndrome ... #APS #management ... #hematology #treatment
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... vasculitis) • Cutaneous ... Leukemia, Lymphoma Ocular ... #diagnosis #management ... signs #symptoms #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
involvement: May involve anterior ... sites such as the collar ... #Rheumatology # ... diagnosis #management ... #Dermatology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
gangrenosum • Cutaneous ... capillary leak syndrome ... Hyperviscosity syndrome ... Hypergammaglobulinemic macular ... Paraproteinemias #Hematology