279 results
Diagnosis of IgA Vasculitis (Henoch-Schönlein Purpura) - French Vasculitis Study Group 

1) Suggestive clinical manifestations
Diagnosis of IgA Vasculitis ... Purpura) - French Vasculitis ... dominant immune deposits ... - Dominant IgA deposits ... with vascular IgA deposits
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... SLE, RA related vasculitis ... with IgG/IgM deposits
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Cryoglobulinemia Vasculitis ... 3 types 2) Vasculitis ... cryoglobulin immune deposits ... Vascular occlusion >> vasculitis ... Cryoglobulinemia #Vasculitis
Henoch Schonlein Purpura 
Typically a young boy. Often occurs following upper respiratory tract infection. A systemic
A systemic vasculitis ... dominant immune deposits
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... , small-vessel vasculitis ... lack of immune deposits ... Levamisole-induced vasculitis ... ANCA #Associated #Vasculitis
IgA Vasculitis – Henoch Scholein Purpura: Pathogenesis and Clinical Findings

 - Infectious Agents - 50% have
IgA Vasculitis – ... complexes, which then deposit ... Leukocytoclastic vasculitis ... Cutaneous small vessel vasculitis ... #HSP #IgA #Vasculitis
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
leading to the deposit ... • IgA vasculitis ... Hypersensitivity vasculitis ... • Vasculitis ... #rheumatology #vasculitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... When to Consider Vasculitis ... abnormalities Vasculitis ... Symptoms (SX) in Vasculitis ... nephropathy, IgA (cmpkx deposits
Polyarteritis Nodosa (PAN): Pathogenesis and Clinical Findings

Medical Comorbidities Malignancies (most commonly hairy-cell leukemia)
Immunogenetic Predisposition: patient is
antigen-antibody complexes deposit ... Signs #Symptoms #Vasculitis
Lupus (SLE): Mucocutaneous Manifestations

 • Langerhan cells and keratinocytes release cytokines -> localized inflammatory response ->
immunoglobulin deposit ... Livedo Reticularis, Vasculitis