1526 results
Inherited Defects in Kidney Tubule Epithelial Cells

Renal glucosuria - Na+-dependent glucose cotransporter
Cystinuria - Amino acid transporter
Bartter
limb Gitelman syndrome ... tubule Liddle syndrome ... cell epithelial sodium ... of epithelial sodium ... Nephrogenic diabetes insipidus
Hypernatremia - Differential Diagnosis Workup Algorithm

1) Check Urine Osmolality:
 > 600 mOsm/kg - Implies extrarenal mechanism
Euvolemic: Diabetes insipidus ... Hypervolemic: Conn syndrome ... , Cushing syndrome ... Algorithm #nephrology #sodium
Diabetes Insipidus vs Syndrome of Inappropriate ADH (SIADH) - Comparison Table

Diabetes Insipidus - Inadequate ADH
SIADH -
Diabetes Insipidus ... vs Syndrome of ... Table Diabetes Insipidus ... #Diabetes #Insipidus
Hypernatremia Differential Diagnosis Algorithm - Diabetes Insipidus Workup

Step #1 - Consider the history
Step #2 - Assess
Algorithm - Diabetes Insipidus ... Management #Algorithm #Sodium ... #nephrology #insipidus
Causes of Hypernatremia - Differential Diagnosis
Inadequate water intake:
 • Lack of access to water
Extrarenal hypotonic fluid
Central diabetes insipidus ... Nephrogenic diabetes insipidus ... Causes #nephrology #sodium
Etiologies of Hypernatremia - Differential Diagnosis
GI losses / Insensible losses
Sodium Overload
Transcellular Movement of Water
Central Diabetes Insipidus
Insensible losses Sodium ... Central Diabetes Insipidus ... Nephrogenic Diabetes Insipidus
Causes of Hypernatremia - Differential Diagnosis Algorithm
Hypernatremia - Excess free water loss, Serum Sodium >145 mmol/L
High
water loss, Serum Sodium ... kg • Diabetes Insipidus
Wolfram syndrome (WS) is a form of monogenic diabetes that typically presents with diabetes mellitus in
Wolfram syndrome ... develop diabetes insipidus ... DIDMOAD (Diabetes Insipidus
Water Deprivation Test - Differential Diagnosis of Diabetes Insipidus (DI)
Concept of WDT: endogenous vasopressin secretion is
Diagnosis of Diabetes Insipidus ... capacity #Diabetes #Insipidus
Brugada syndrome with non-sustained VT; sodium channel blocking drugs (e.g. amio, procainamide) can be dangerous here!

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Brugada syndrome ... non-sustained VT; sodium ... amalmattu #Brugada #syndrome