54 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Manifestations of Granulomatosis ... involvement in granulomatosis ... GPA causes disease ... reticularis Differential ... rash #diagnosis #rheumatology
Common Variable Immunodeficiency (CVID)

What?
CVID: Immunodeficiency disorder with hypogammaglobulinemia -> increased infection risk secondary to impaired B-cell
breast cancer Granulomatous ... severe community-acquired ... and M panel Management ... hypogammaglobulinemia #immunology #hematology ... #diagnosis #management
Classification of Diabetes Insipidus

Central or neurogenic diabetes insipidus:
 - Congenital - Structural malformations affecting the hypothalamus
precursor protein - Acquired ... Histiocytosis and granulomatous ... AQP-2 gene - Acquired ... insipidus: - Acquired ... Nephrology #Diagnosis #Differential
Summary of Coagulation Deficiencies
Inherited:
 • Hemophilia A - Deficiency of Factor VIII
 • Hemophilia B -
Summary of Coagulation ... of Factor IX Acquired ... Malabsorption (e.g. celiac disease ... Advanced Liver Disease ... #Deficiencies #Summary
Causes of Bleeding / Bruising - Differential Diagnosis Algorithm
Thrombocytopenia - Quantitative Defect
 • Decreased Production
 •
Bleeding / Bruising - Differential ... Vascular System - Acquired ... Coagulation Proteins - Acquired ... Bleeding #Bruising #Differential ... Algorithm #Causes #Hematology
Acquired von Willebrand Syndrome - Diagnosis and Management
 • Autoantibodies to vWF: Lymphoproliferative disorders (e.g. lymphoma,
Acquired von Willebrand ... Diagnosis and Management ... thrombocythemia), Autoimmune disease ... #treatment #hematology ... #differential
Causes of Splenomegaly - Differential Diagnosis Algorithm
Infectious
 • Bacterial
 • Viral (EBV)
 • Parasitic
 • Fungal
Congestive
Splenomegaly - Differential ... • Gaucher's Disease ... Spherocytosis • Acquired ... Spleen #Enlarged #Differential ... Algorithm #Causes #Hematology
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
Erythematosus - Summary ... with more severe disease ... Erythematosus #SLE #Summary ... #diagnosis #rheumatology ... #management
Erythrocytosis - Polycythemia Differential Diagnosis Algorithm

Elevated Hemoglobin:
 • Males: Hb > 16.5 g/dL/HCT ≥ 49%
 •
- Polycythemia Differential ... Polycythemia - Acquired ... Cardiac/pulmonary disease ... Polycythemia #Vera #PV #Differential ... Diagnosis #Algorithm #hematology
Elevated Lactate Dehydrogenase (LDH) - Differential Diagnosis Framework

LDH is a cytoplasmic enzyme present in tissues throughout
Dehydrogenase (LDH) - Differential ... cell enzymes - Acquired ... Myopathies (inherited, acquired ... • Eosinophilic granulomatosis ... polyangiitis • Granulomatosis