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Thrombotic Microangiopathies In Systemic Lupus Erythematosus

Dr. Laurent ARNAUD @Lupusreference

#TMAs #Thrombotic #Microangiopathies #Systemic #Lupus #Erythematosus #SLE #hematology
Microangiopathies In Systemic ... Lupus Erythematosus ... #SLE #hematology ... #differential #diagnosis ... #causes
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Lupus (SLE) General ... syndromes Heart (25%): Pericarditis ... #SLE #systemic ... erythematosus #signs ... #symptoms #diagnosis
Systemic Lupus Erythematosus (SLE): Musculoskeletal Manifestations

 • Immune Complex Deposition
    - Arthralgia, Arthritis
Systemic Lupus Erythematosus ... (SLE): Musculoskeletal ... Myopathy (Also caused ... pathophysiology #signs ... #symptoms #diagnosis
Systemic Lupus Erythematosus (SLE) - Typical Signs/Symptoms
Alopecia, Fever, Malar rash, Photosensitivity, Adenopathies, Lupus pneumonia, Pleurisy, Pancreatitis,
Systemic Lupus Erythematosus ... (SLE) - Typical ... ulcers, Rash, Pericarditis ... #SLE #Signs #Symptoms ... #diagnosis #rheumatology
Causes of Pericarditis - Differential Diagnosis Algorithm
Viral:
 • Coxsackie
 • Echovirus
 • Adenovirus
 • Epstein-Barr virus
Causes of Pericarditis ... - Differential Diagnosis ... arthritis • Systemic ... lupus erythematosus ... #Cardiology
Top 10 situations when to think about lupus
1) Inflammatory joint pain (especially in the wrists and
many differential diagnoses ... 4) Always with pericarditis ... children (pediatric SLE ... #diagnosis #sle ... #clues #system
Constrictive Pericarditis on POCUS Echocardiogram - Apical 3-Chamber View

Young Lupus patient admitted to hospital new onset
View Young Lupus ... What do you see ... Lupus pericarditis ... Had diagnostic tap-fever ... Echocardiogram #clinical #cardiology
Features That Differentiate Acute Pericarditis from Myocardial Ischemia or Infarction and Pulmonary Embolism

In contrast to the
presentation of systemic ... lupus erythematosus ... life-threatening causes ... #Signs #Presentation ... comparison #Table #Diagnosis
Kussmaul's Sign - Differential Diagnosis

Typically the JVP decreases with inspiration as the negative intrathoracic pressure "sucks
- Differential Diagnosis ... with constrictive pericarditis ... conditions where we may see ... #cardiology #differential ... #causes
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
Episcleritis Signs ... Causes: - Idiopathic ... ’s syndrome - Lupus ... Sweet #Syndrome #diagnosis ... #dermatology #oncology