Dr. Gerald Diaz @GeraldMD
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Board Certified Internal Medicine Hospitalist, GrepMed Editor in Chief πŸ‡΅πŸ‡­ πŸ‡ΊπŸ‡Έ - Sign up for an account to like, bookmark and upload images to contribute to our community platform. Follow us on IG: https://www.instagram.com/grepmed/ | Twitter: https://twitter.com/grepmeded/
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Von Willebrand Disease - Clinical Presentation, Diagnosis and Management

- Dr. Eric Strong @DrEricStrong - Strong Medicine
Von Willebrand Disease ... - Clinical Presentation ... VonWillebrand #Disease ... Diagnosis #Management #hematology ... #treatment
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
Non-HCV infectious ... cryoglobulinemia vasculitis Clinical ... neuropathy Treatment ... with refractory disease ... Cryoglobulinemia #Vasculitis #Rheumatology
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash Β± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... Diaqnoses: β€’ Infectious ... diagnosis #management #treatment ... #rheumatology
Aplastic Anemia - Illness Script
Signs and symptoms:
 β€’ Recurrent infections from neutropenia
 β€’ Mucosal bleeding from
: β€’ Recurrent infections ... megaloblastic anemia Treatment ... (transfusions, antibiotics ... diagnosis #management #treatment ... #hematology
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 β€’ Mechanical Trauma (Microangiopathic hemolytic anemia):
cold agglutin disease ... Mycoplasma pneumoniae infection ... Drugs (Beta lactam antibiotics ... spherocytosis) β€’ Infections ... differential #diagnosis #hematology
Summary of Coagulation Deficiencies
Inherited:
 β€’ Hemophilia A - Deficiency of Factor VIII
 β€’ Hemophilia B -
malnutrition, Antibiotics ... Malabsorption (e.g. celiac disease ... Advanced Liver Disease ... Deficiencies #Summary #table ... comparison #diagnosis #hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)β†’Activation of CD8 T cells (IFN-y) β†’ Excessive activation of macrophages
accumulation of clinical ... Assessment β€’ Clinical ... β€’ Autoimmune diseases ... Unknown cause Treatment ... #summary #rheumatology
Von Willebrand Disease - Most common inherited bleeding disorder 
Clinical 
 β€’ Easy bruising 
 β€’
Von Willebrand Disease ... bleeding disorder Clinical ... factor VIII) Treatment ... VonWillebrand #Disease ... #Diagnosis #Hematology
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
: Overwhelming clinical ... age, however the disease ... : β€’ Infection ... rapidly, and empiric antibiotic ... #hematology
Adult-Onset Still's Disease (AOSD)
Rare inflammatory disorder of unknown etiology, difficult to diagnose because of heterogenous presentation.
Adult-Onset Still's Disease ... conditions (autoimmune, infectious ... susceptibility, infectious ... synovitis (40%) Treatment ... #AOSD #rheumatology