Dr. Gerald Diaz @GeraldMD
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Board Certified Internal Medicine Hospitalist, GrepMed Editor in Chief πŸ‡΅πŸ‡­ πŸ‡ΊπŸ‡Έ - Sign up for an account to like, bookmark and upload images to contribute to our community platform. Follow us on IG: https://www.instagram.com/grepmed/ | Twitter: https://twitter.com/grepmeded/
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Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)β†’Activation of CD8 T cells (IFN-y) β†’ Excessive activation of macrophages
accumulation of clinical ... Assessment β€’ Clinical ... β€’ Autoimmune diseases ... Treatment: β€’ ... #summary #rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
: Overwhelming clinical ... age, however the disease ... can mimic common infections ... : β€’ Infection ... #hematology
Hemophagocytic Lymphohistiocytosis (HLH) Treatment
Primary HLH:
 - HLH-94 Protocol
    β€’ Dexamethasone
) Treatment Primary ... associated with infection ... or autoimmune disease ... for refractory disease ... #hematology
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
vasculitis - Diagnosis, causes ... cryoglobulinemia vasculitis Clinical ... neuropathy Treatment ... with refractory disease ... Cryoglobulinemia #Vasculitis #Rheumatology
Clarkson’s Disease - Capillary leak syndrome
Epidemiology: Roughly 150 published cases, Median age 50 years, No sex
- Capillary leak ... Relapsing-remitting course +++ Clinical ... of infections) ... #Capillary #leak ... #rheumatology
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Gammopathy of Clinical ... Differential Diagnosis Neurologic-Centered ... : β€’ Systemic capillary ... Ig deposition disease ... Differential #Diagnosis #hematology
Secondary Syphilis Rash
Secondary syphilis is the most contagious of all the stages of this disease, and
, but without treatment ... , the infection ... resembling rashes caused ... Rash #Diagnosis #Clinical ... #Photo #Dermatology
TRALI vs TACO - Transfusion Reactions
TRALI:
 β€’ Epidemiology: 0.1% of transfused patientsl
 β€’ Risk factors: Critical
Risk factors: Critical ... without other cause ... : 33% β€’ Treatment ... Transfusion #Reactions #hematology ... diagnosis #comparison #table
Chronic Lymphocytic Leukemia (CLL) - Summary
Overview: 
 β€’ Most common leukemia in adults
 β€’ Disorder of
immunophenotype Clinical ... Complications: 1) Infection ... transformation) Treatment ... chemotherapy for low-risk disease ... Leukemia #oncology #hematology
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 β€’ Epidemiology: -10% of all lupus cases, drug-dependent,
to 1:1 F:M β€’ Clinical ... Discontinuation of causal ... Evolution: Chronic disease ... sle #comparison #table ... #rheumatology #