259 results
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Features: POEMS, AL amyloid ... capillary leak syndrome ... • Schnitzler syndrome ... • Organized Ig deposits ... : Ig-related amyloid
Nephrotic Syndrome - Classification
 - Podocytopathies
 - Immunocomplex Deposits 
 - Other substances Deposits 

#Nephrotic #Syndrome
Nephrotic Syndrome ... Immunocomplex Deposits ... Other substances Deposits ... #Nephrotic #Syndrome
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Extravascular lg Deposits ... Intravascular lg deposits ... secretion: POEMS syndrome ... , Syndrome Schnitzler ... cutis laxa, TEMPI syndrome
Hypocalcemia - Diagnosis and Management
PTH Independent (↑ PTH)
 • LOW VIT D
    -
Diagnosis and Management ... Formation: Hungy Bone Syndrome ... Infiltrative: Amyloid ... - DiGeorge Syndrome ... Hypocalcemia #Diagnosis #Management
Priapism 

Secondary Causes:
Medications- intracavernosal injections, anticoagulants, PDE5 inhibitors, alpha blockers, methylphenidate, cocaine
Any hyperviscosity syndrome (SCD, leukemia,
hyperviscosity syndrome ... or are zebras (…amyloid ... Priapism #Diagnosis #Management
Membranoproliferative Glomerulonephritis (MPGN) AKA: Mesangiocapillary GN
 • Active Urine Sediment (dysmorphic RBC, RBC casts, +/- proteinuria)
glomerulopathy (Dense deposit ... Minimal immune deposits ... anti-phospholipid syndrome
Great Mimickers - SHALLOTS Mnemonic

S- Syphilis - Neurosyphilis, aortitis, gummas... Granulomas can form anywhere! Skin, mucosa,
A - Amyloid - Amyloid ... deposits everywhere
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Amyloidosis: • Primary amyloid ... : • Nephrotic syndrome ... Bone/Joint: • Amyloid ... Carpal tunnel syndrome ... (AMYLOID ANGIOPATHY
This image shows spicular amyloid deposits showing blunt conical formations with interconnecting fibrils.

Dr. Stephen Bonsib via
shows spicular amyloid ... deposits showing ... arkanalabs #amyloid ... #deposits #deposition
Inherited Colorectal Cancer (CRS) Syndromes
Adenomatous Polyposis Syndromes:
 • Familial Adenomatous Polyposis (FAP), Attenuated FAP (AFAP), MUTYH
Colorectal Cancer (CRS) Syndromes ... Adenomatous Polyposis Syndromes ... Urinary → Lynch Syndrome ... Peutz-Jeghers Syndrome ... #diagnosis #management