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Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Non-hepatitis C virus Cryoglobulinemia ... MONOCLONAL CRYOGLOBULINEMIA ... #Vasculitis #Management ... #Rheumatology # ... Monoclonal #Mixed #Cryoglobulinemic
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... Hyperviscosity syndrome ... MIXED CRYOGLOBULINEMIA ... Vasculitis #Diagnosis #Rheumatology ... #Cryoglobulinemic
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... decr of C3 and C4 ... #Vasculitis #Management ... #Rheumatology # ... Cryoglobulinemic
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... Diagnosis, causes and management ... < 5% of mixed cryoglobulinemia ... #Vasculitis #Rheumatology ... #Diagnosis #Management
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Hyperviscosity Syndrome ... Syndrome: • Clinical ... syndrome in 80% ... • Low serum C4 ... classification #rheumatology
Raynaud Phenomenon Differential Diagnosis:

Rheumatologic

 - MCC systemic sclerosis, RA, SLE, Sjogren syndrome, Antisynthetase syndrome, MCTD
Heme

 -
Differential Diagnosis: Rheumatologic ... , SLE, Sjogren syndrome ... Antisynthetase syndrome ... MCTD Heme - Cryoglobulinemia ... Carpal tunnel syndrome
Algorithm for the management of children with nephrotic syndrome and steroid resistant nephrotic syndrome (SRNS)

#nephrotic #syndrome
Algorithm for the management ... with nephrotic syndrome ... resistant nephrotic syndrome ... #nephrotic #syndrome ... nephrology #peds #pediatrics
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Mnemonic C - Cryoglobulinemia ... antiphospholipid syndrome ... #differential #hematology
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
POEMS, AL amyloid, Cryoglobulinemia ... capillary leak syndrome ... • Schnitzler syndrome ... • Cryoglobulinemia ... Differential #Diagnosis #hematology
Top tips for triaging and treating kids with Pitt Hopkins Syndrome
#Diagnosis #Management #PatientInfo #Peds #Pediatrics #PittHopkins
with Pitt Hopkins Syndrome ... #Diagnosis #Management ... PatientInfo #Peds #Pediatrics ... #PittHopkins #Syndrome