11 results
Krabbe Disease 

Check out this interesting case of Krabbe disease, a rare genetic leukodystrophy. Diagnosis was
Diagnosis was made ... • Symmetric abnormal ... #Disease #Diagnosis ... #MRI #Clinical ... #Radiology
Myocarditis
Diagnosis 
• Endomyocardial biopsy (gold standard, rarely performed) 
• Clinical presentation 
• Cardiovascular MRI 
Clinical 
•
Myocarditis Diagnosis ... Cardiovascular MRI ... summation gallop • Abnormal ... #Myocarditis #Diagnosis ... #Management #Cardiology
LUMBAR Syndrome

What do you call a segmental lumbosacral hemangioma + spinal problems?? LUMBAR syndrome, a fairly
ensure correct management ... malformation & Arterial ... spine + MRI/MRA ... LUMBAR #Syndrome #Radiology ... #Diagnosis #Clinical
Peripartum Cardiomyopathy - Summary
1. Definition
 • Towards the end of pregnancy to 5 months postpartum
Differential Diagnosis ... ancestry, LGE on MRI ... sx overlap with normal ... Serial TTE and close ... #diagnosis #management
Cardiac Amyloid - Diagnosis, Signs, Symptoms and Management

Clinical Presentation
- exertional dyspnea
- peripheral edema
- exertional syncope
- peripheral
Cardiac Amyloid - Diagnosis ... Clinical Presentation ... hepatomegaly - normal ... precordial leads) - atrial ... Amyloidosis #Cardiac #Diagnosis
Haglund Syndrome - MSK Radiology
Imaging Findings:
 • The Haglund Deformity (enlarged superior margin calcaneal posterior process)
Syndrome - MSK Radiology ... bursa is commonly abnormal ... Differential diagnosis ... #mri #clinical ... #Radiology #diagnosis
Guillain-Barre Syndrome - Summary

Acute AIDP that presents with rapidly progressive flaccid weakness

Epidemiology:
 • 1-2 cases/100,000 per
tachycardia, reversible cardiomyopathy ... Guillain-Barre Diagnosis ... axonal form • MRI ... Barre #Syndrome #diagnosis ... #management #treatment
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Clinical suspicion ... Amyloidosis Clinical ... & restrictive cardiomyopathy ... disproportionate atrial ... enlargement • MRI
Accordion Sign of Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) on Cardiac MRI
30-year old woman with VPCs. Diagnosis?
Classic
Right Ventricular Cardiomyopathy ... ARVC) on Cardiac MRI ... Diagnosis? ... interspersed with more normal ... #clinical #cardiology
►
Peripartum Cardiomyopathy (PPCM)

What is PPCM?
• A form of acute systolic heart failure that develops late in
Cesarean delivery Clinical ... Presentation: • Mimics normal ... Key Point: High clinical ... recognition and management ... #Cardiology #OBGyn