13 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Vasculitis - French ... Vasculitis Study ... lenalinomide MIXED ... #Rheumatology # ... Monoclonal #Mixed
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
Non-HCV infectious mixed ... cryoglobulinemia ... Group < 5% of mixed ... #Vasculitis #Rheumatology ... #Mixed #Cryoglobulinemic
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Vasculitis 1 ... 3 types 2) Vasculitis ... Hyperviscosity syndrome MIXED ... #Vasculitis #Diagnosis ... #Rheumatology #
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
involvement in 35% of mixed ... cryoglobulinemia ... vasculitis Associated ... #Vasculitis #Management ... #Rheumatology #
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
, in Mixed Cryoglobulinemia ... seen with the mixed ... Etiology - Mixed ... diagnosis #types #classification ... #rheumatology #
Cryoglobulinemia Classification Types

Type 1: Monoclonal IgM (rarely IgG/lgA)
 • Raynaud phenomenon, Digital ulcers/gangrene, Livedo reticularis, Hyperviscosity
Cryoglobulinemia ... Classification ... IgM > 4 g/dL) Mixed ... #Classification ... #Types #hematology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... Vasculitis Vasculitis ... scleroderma - mixed ... dermatomyositis #Size #Classification ... #Diagnosis #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
ANCA +MPO) • Cryoglobulinemic ... Complement (Low levels mixed ... cryoglobulinemia ... differential #diagnosis #rheumatology ... #classification
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
• Ig A vasculitis ... /HSP • Cryoglobulinemia ... (MIXED) • ANCA ... Differential #Diagnosis #hematology ... #rheumatology #
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... purpura (16%) • Painful ... Henoch-Schönlein purpura • Mixed ... cryoglobulinemia ... rash #diagnosis #rheumatology