65 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Vasculitis - French ... Vasculitis Study ... /or refractory disease ... #Vasculitis #Management ... #Rheumatology #
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
, causes and management ... vasculitis Clinical ... with refractory disease ... #Vasculitis #Rheumatology ... #Diagnosis #Management
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Vasculitis 1 ... not related to clinical ... 3 types 2) Vasculitis ... #Vasculitis #Diagnosis ... #Rheumatology #
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... vasculitis Associated ... #Vasculitis #Management ... #Rheumatology # ... Cryoglobulinemic
The Associated Diseases of Cryptoglobulinemia Vasculitis
#rheumatology #causes
The Associated Diseases ... of Cryptoglobulinemia ... Vasculitis #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... Urticarial/LCV) - Cryoglobulinemic ... : • Behcet Disease ... #skin #dermatology ... #rheumatology #
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Connective tissue disease ... hemopathies (4%) • Cryoglobulinemia ... vasculitis (3%) ... #dermpath #dermatology ... lesions #diagnosis #clinical
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Cryoglobulinemia ... Syndrome: • Clinical ... • Autoimmune diseases ... classification #rheumatology ... #vasculitis
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- Bone marrow disease ... deficiency • Liver disease ... Von Willebrand disease ... /HSP • Cryoglobulinemia ... Differential #Diagnosis #hematology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
ANCA +MPO) • Cryoglobulinemic ... (Granulomatous disease ... atherosclerotic disease ... Low levels mixed cryoglobulinemia ... differential #diagnosis #rheumatology