12 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Non-hepatitis C virus Cryoglobulinemia ... MONOCLONAL CRYOGLOBULINEMIA ... /or refractory disease ... #Vasculitis #Management ... Monoclonal #Mixed #Cryoglobulinemic
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... < 5% of mixed cryoglobulinemia ... vasculitis Clinical ... #Vasculitis #Rheumatology ... #Mixed #Cryoglobulinemic
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
deposits: Type I cryoglobulinemia ... activity: Type II cryoglobulinemia ... Cold agglutinin disease ... manifestations #dermatology ... #skin #clinical
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Cryoglobulinemia ... , in Mixed Cryoglobulinemia ... Triad - Mixed Cryoglobulinemia ... Syndrome: • Clinical ... • Autoimmune diseases
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... Urticarial/LCV) - Cryoglobulinemic ... : • Behcet Disease ... #skin #dermatology ... #rheumatology #
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Connective tissue disease ... hemopathies (4%) • Cryoglobulinemia ... vasculitis (3%) ... #dermpath #dermatology ... lesions #diagnosis #clinical
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- Bone marrow disease ... Von Willebrand disease ... /HSP • Cryoglobulinemia ... Differential #Diagnosis #hematology ... #nonpalpable #dermatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Dermatologic Manifestations ... Rarely dominate the clinical ... purpura • Mixed cryoglobulinemia ... #Dermatologic ... Polyangiitis #GPA #dermatology
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Gammopathy of Clinical ... POEMS, AL amyloid, Cryoglobulinemia ... Schnitzler syndrome • Cryoglobulinemia ... Ig deposition disease ... Differential #Diagnosis #hematology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... , sepsis or cryoglobulinemia ... Diagnosis: • + Clinical ... Calciphylaxis • Cryoglobulinemia ... #hematology