12 results
Myositis and Myopathies
Polymyositis 
 • Progressive, symmetric muscle weakness 
 • Elevated CK, +Anti-Jo, +Anti-Mi2
Dermatomyositis
Myositis and Myopathies ... Polymyositis • Progressive ... Dermatomyositis • Progressive ... Myopathies #myopathy #differential ... diagnosis #comparison #rheumatology
Systemic Sclerosis Associated Autoantibodies
Anti-topoisomerase I (anti-Sc170): Diffuse skin disease, Pulmonary fibrosis
Anti-centromere: Limited skin disease (~93-95%), Pulmonary
skin disease, Pulmonary ... disease (~93-95%), Pulmonary ... crisis, Rapid progressive ... Anti-PM-Sc1: Overlap myositis ... Autoantibodies #diagnosis #rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Rapidly Progressive ... With associated pulmonary ... RPGN #Rapidly #Progressive ... #diagnosis #algorithm ... #rheumatology
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... Syndromes and Mimics - Differential ... hemorrhage + rapidly progressive ... , Inflammatory Myositis ... Kumfer @AnnKumfer #Pulmonary
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
vasculopathy and progressive ... calcinosis • Pulmonary ... disease), PAH (pulmonary ... acro-osteolysis, myositis ... Scleroderma #SSc #rheumatology
Causes of Peripheral Weakness without Sensory Changes - Differential Diagnosis Algorithm
No Objective Weakness
 • Cardio-pulmonary disease
Sensory Changes - Differential ... Diagnosis Algorithm ... Weakness • Cardio-pulmonary ... Lead toxicity • Progressive ... #Diagnosis #Algorithm
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Lung Disease - Differential ... Diagnosis Algorithm ... Pneumonia - slowly progressive ... leaking out of pulmonary ... #Diagnosis #Algorithm
Lymphomas and Lymphoproliferative Disorders - Differential Diagnosis Algorithm
Hodgkin Lymphoma ~40% - Characteristic For Reed-Sternberg (RS) Cells
Lymphoproliferative Disorders - Differential ... Diagnosis Algorithm ... system (node) with progression ... pathophysiology #Hematology ... #algorithm
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... proteinuria, Rapidly progressing ... is 50 years • Progressive ... immune GN (rapidly progressive ... #Diagnosis #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitides - Differential ... proteinuria, rapidly progressing ... GN • New pulmonary ... Conjunctivitis, mucositis ... #diagnosis #rheumatology