1146 results
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Systemic Sclerosis (Scleroderma ... 3 Subtypes of Scleroderma ... Sclerosis sine scleroderma ... calcinosis • Pulmonary ... disease), PAH (pulmonary
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
Tissue Disease: RA, Scleroderma ... lung #disease #pulmonary
Diagnostic Criteria for Scleroderma Renal Crisis 

1. New onset blood pressure >150/85 mm Hg OR increase
Diagnostic Criteria for Scleroderma ... anuria - Flash pulmonary ... shrinkage #Scleroderma
Antinuclear Antibodies (ANA)
ANA or Anti-NucIear Antibody refers to antibodies against antigens in the nucleus → like
systemic sclerosis/scleroderma ... systemic sclerosis/scleroderma ... Systemic sclerosis/scleroderma ... Systemic Sclerosis (scleroderma ... , Interstitial Pulmonary
Hilar and mediastinal lymphadenopathy
In sarcoidosis the common pattern is right paratracheal and bilateral hilar adenopathy ('1-2-3-sign').
In
blastomycosis and scleroderma ... Diagnosis #Radiology #Pulmonary
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... Complement Levels: Scleroderma ... Kumfer @AnnKumfer #Pulmonary
High-Res Chest CT Patterns - Differential Diagnosis Framework
Reticular:
 • Septal Thickening: Lymphangitic Carcinoma, Interstitial Edema, Alveolar
Honeycombing: Idiopathic Pulmonary ... Fibrosis, RA, Scleroderma ... Differential #Diagnosis #pulmonary
Diffuse Systemic Sclerosis (Scleroderma)
 - Pulmonary Fibrosis -> Crackles, Abnormal CXR
 - Pulmonary Hypertension, Right Heart
Systemic Sclerosis (Scleroderma ... ) - Pulmonary ... Abnormal CXR - Pulmonary ... SystemicSclerosis #Scleroderma
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Lymphangioleiomyomatosis (LAM), • Pulmonary ... leaking out of pulmonary ... Systemic Lupus and Scleroderma
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
Wilson's disease Pulmonary ... Spondyloarthropathies, SLE • Pulmonary ... Telangiectasia • Scleroderma ... Thickened skin • Scleroderma