668 results
Systemic Sclerosis (Scleroderma)
Limited - CREST:
 • Calcinosis
 • Raynaud phenomenon
 • Esophageal dysmotility
 • Sclerodactyly
 •
Systemic Sclerosis (Scleroderma ... 10% - 15% • Scleroderma ... renal crisis ... Systemic #Sclerosis #Scleroderma
Management of Scleroderma Renal Crisis

#Scleroderma #Renal #Crisis #Management #Algorithm #Rheumatology
Management of Scleroderma ... Renal Crisis ... #Scleroderma #Renal
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
Systemic Sclerosis (Scleroderma ... 3 Subtypes of Scleroderma ... Sclerosis sine scleroderma ... arterial HTN) • Renal ... : scleroderma renal
Diagnostic Criteria for Scleroderma Renal Crisis 

1. New onset blood pressure >150/85 mm Hg OR increase
Diagnostic Criteria for Scleroderma ... Renal Crisis ... A decline in renal ... shrinkage #Scleroderma ... #Renal #Crisis
Hypertension and Altered Mental Status (AMS) - Differential Diagnosis Framework

Hypertension:
 • Hypertensive emergency
 • Hypertensive encephalopathy
Pre-Eclampsia Renal ... Acute/Chronic renal ... failure • Renal ... Polyarteritis nodosa • Scleroderma ... renal crises
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... Complement Levels: Scleroderma ... Renal Crisis, IgA ... AnnKumfer #Pulmonary #Renal
Scleroderma Renal Crisis (SRC)

Clinical Presentation of Scleroderma Renal Crisis:
1) Acute kidney injury
2) Abrupt onset of hypertension
3)
Scleroderma Renal ... Presentation of Scleroderma ... Renal Crisis: ... MithuRheum #SRC #Scleroderma ... #Renal #Crisis
Differential diagnosis of schistocytes / fragmentation hemolysis:
 • Thrombotic microangiopathies (TMA)
    - TTP
hypertension • Scleroderma ... renal crisis •
Scleroderma Renal Crisis - Diagnosis and management

Diaqnosis
 • De novo arterial hypertension of normotensive form +++
Scleroderma Renal ... nephrologist • Renal ... TerrierBen #Scleroderma
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
Systemic sclerosis (scleroderma ... polyangiitis without renal ... ANCA+ 30-60% • Renal-limited