9 results
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology ... Hypocomplementemic Urticarial Vasculitis ... Formation -> Vasculitis ... #HUV #Pathophysiology ... #Rheumatology
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis ... cryoglobulinemia vasculitis ... relapsing patients are frequently ... anti-infectious agents are frequently ... #Rheumatology #
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... , small-vessel vasculitis ... 100%, PR3+ 50%, frequently ... ANCA #Associated #Vasculitis ... PR3 #Diagnosis #Rheumatology
Diagnosis of IgA Vasculitis (Henoch-Schönlein Purpura) - French Vasculitis Study Group 

1) Suggestive clinical manifestations
Diagnosis of IgA Vasculitis ... Purpura) - French Vasculitis ... common systemic vasculitis ... occurring most frequently ... HSP #Diagnosis #Rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
three primary pathophysiologic ... Glomerulonephritis #Vasculitis ... diagnosis #algorithm #rheumatology
Frequency of ANCA Positivity in Different Conditions
ANCA-Associated Vasculitis
 • GPA - PR3-ANCA 75%, MPO-ANCA 20%, 5%
Frequency of ANCA ... ANCA-Associated Vasculitis ... Renal-limited vasculitis ... • Drug-induced vasculitis ... PR3 #diagnosis #rheumatology
Venous Thrombosis vs Arterial Thrombosis - Differential Diagnosis Framework

VENOUS THROMBOSIS

 • Acquired Risk Factors:
	- >48 hours
19 - PNH - Vasculitis ... Venous #Arterial #pathophysiology ... #hematology #differential
Giant cell arteritis (GCA)

Giant cell arteritis (GCA) definition: Most common systemic inflammatory vasculitis in older adults
systemic inflammatory vasculitis ... complications frequently ... differential diagnosis = vasculitis ... them, but urgent rheumatology
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
ANCA-associated vasculitis ... cell lymphoma Pathophysiology ... diagnosis #management #rheumatology