40 results
Von Willebrand Disease - Most common inherited bleeding disorder 
Clinical 
 • Easy bruising 
 •
Von Willebrand Disease ... bleeding disorder Clinical ... bruising • Skin ... factor VIII) Treatment ... #Diagnosis #Hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... injury) • Neurologic ... oral ulcers in 12 ... Arthritis, AS Treatment ... #rheumatology #
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
Clinical manifestations ... - Skin involvement ... neuropathy Treatment ... with refractory disease ... #Rheumatology #
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... , neurologic, and ... • Progressive symptoms ... cognitive impairment, neurologic ... Differential #Diagnosis #Rheumatology
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
episodes within a 12 ... Uveitis or retinal vasculitis ... - Skin lesions ... test Most Common Clinical ... Wide variety of skin
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Somatic) Syndrome Clinical ... Syndrome: • Common Clinical ... nose chondritis, skin ... thromboembolic disease ... recurrent fevers, vasculitis
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Symptoms ... malignancies, vasculitis ... Cryofibrinogenemia Clinical ... Diagnosis: • + Clinical ... #hematology
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Clinical Features ... Sjögrens (15%) Skin ... Butterfly rash, Vasculitis ... pain (20%) Renal disease ... erythematosus #signs #symptoms
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
with systemic disease ... symptoms by days ... , breast CA - Hematologic ... Leukocytoclastic vasculitis ... Treatment: - Systemic
Chronic Lymphocytic Leukemia (CLL) - Summary
Overview: 
 • Most common leukemia in adults
 • Disorder of
immunophenotype Clinical ... Splenomegaly 5) Symptoms ... chemotherapy for low-risk disease ... Constitutional symptoms ... Leukemia #oncology #hematology