13 results
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
: • Primary amyloid ... • Heavy-chain (AH ... Clinical suspicion ... Clinical Manifestations ... (AMYLOID ANGIOPATHY
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Extravascular lg Deposits ... : Systemic amyloidosis ... , Nodular amyloidosis ... Intravascular lg deposits ... dermatology #skin #clinical
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Gammopathy of Clinical ... Features: POEMS, AL amyloid ... • Organized Ig deposits ... : Ig-related amyloid ... Monoclonal #Gammopathy #Clinical
This image shows spicular amyloid deposits showing blunt conical formations with interconnecting fibrils.

Dr. Stephen Bonsib via
shows spicular amyloid ... deposits showing ... arkanalabs #amyloid ... #deposits #deposition ... ElectronMicroscopy #SEM #clinical
Macroglossia in Light-Chain Amyloidosis- Physical examination revealed macroglossia, with indentations from the teeth (Panel A)...A biopsy
in Light-Chain Amyloidosis ... light chains are deposited ... AL amyloidosis is ... treatment are critical ... #clinical #photo
Cardiac Amyloidosis Management
The liver produces transthyretin tetramers, which dissociate into monomers and mis-fold, then aggregate into
Cardiac Amyloidosis ... aggregate into amyloid ... fibrils and deposit ... Cardiac amyloidosis ... yeeann_c #Cardiac #Amyloidosis
Cardiac Amyloid - Diagnosis, Signs, Symptoms and Management

Clinical Presentation
- exertional dyspnea
- peripheral edema
- exertional syncope
- peripheral
Cardiac Amyloid ... Management Clinical ... cardionerds #Amyloidosis
This image shows spicular amyloid with tapering conical masses interconnected by branching fibrils!

Dr. Stephen Bonsib via
shows spicular amyloid ... with tapering conical ... arkanalabs #amyloid ... #desposition #deposits ... ElectronMicroscopy #SEM #clinical
This image shows portions of glomerular tuft with collapsed GBM (across top), spicular amyloid (middle right),
top), spicular amyloid ... ), and nodular amyloid ... glomerulus #GBM #amyloid ... #desposition #deposits ... ElectronMicroscopy #SEM #clinical
Restrictive Cardiomyopathy - Diagnosis and Causes
Clinical: Dyspnea, Exercise Intolerance, ↑ "Right Sided-Symptoms" (ascites, hepatomegaly, ↑↑peripheral edema)
Physical
Diagnosis and Causes Clinical ... Infiltrative: Amyloidosis ... (AL Amyloid, Wild