2263 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Treatment of Non-hepatitis ... C virus Cryoglobulinemia ... MONOCLONAL CRYOGLOBULINEMIA ... lenalinomide MIXED CRYOGLOBULINEMIA ... Monoclonal #Mixed #Cryoglobulinemic
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... < 5% of mixed cryoglobulinemia ... neuropathy Treatment ... TerrierBen #NonHCV #Cryoglobulinemia ... Rheumatology #Mixed #Cryoglobulinemic
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... ) MONOCLONAL CRYOGLOBULINEMIA ... syndrome MIXED CRYOGLOBULINEMIA ... TerrierBen #Cryoglobulinemia ... #Rheumatology #Cryoglobulinemic
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... neuropathy • Type II cryoglobulinemia ... #Involvement #Cryoglobulinemia ... #Rheumatology #Cryoglobulinemic
Sjogren's Syndrome Overview

Epidemiology:
• F > M: 9:1
• 5-6th Decades (can be any age)

Autoimmune exocrinopathy multisystemic disease
Disease: • 10%-15% Pulmonary ... , INC risk PE, Pulmonary ... Vasculitis: • 7%, Cryoglobulinemia ... Adenocarcinoma Treatment
Cryoglobulinemia Classification Types

Type 1: Monoclonal IgM (rarely IgG/lgA)
 • Raynaud phenomenon, Digital ulcers/gangrene, Livedo reticularis, Hyperviscosity
Cryoglobulinemia ... peripheral neuopathy, pulmonary ... MatthewHoMD #Cryoglobulinemia
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Cryoglobulinemia ... Mainly in Type I Cryoglobulinemia ... Triad - Mixed Cryoglobulinemia ... with the mixed cryoglobulinemia ... Etiology - Mixed Cryoglobulinemia
Cryoglobulinemia Vasculitis
#rheumatology #diagnosis #signs
Cryoglobulinemia
Treatment Algorithm for Pulmonary Hypertension

#Pulmonary #Hypertension #PAH #Treatment #Management #Algorithm #Medications
Treatment Algorithm ... for Pulmonary Hypertension ... #Pulmonary # ... Hypertension #PAH #Treatment
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
deposits: Type I cryoglobulinemia ... activity: Type II cryoglobulinemia