6012 results
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
Renal involvement ... in 35% of mixed cryoglobulinemia ... min/1.73 m2 at diagnosis ... • Dialysis at diagnosis ... TerrierBen #Renal
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Diagnosis of Cryoglobulinemia ... ) MONOCLONAL CRYOGLOBULINEMIA ... arthritis • Renal ... TerrierBen #Cryoglobulinemia ... #Vasculitis #Diagnosis
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
infectious mixed cryoglobulinemia ... vasculitis - Diagnosis ... < 5% of mixed cryoglobulinemia ... with purpura - Renal ... #Diagnosis #Management
Pulmonary Renal Syndromes and Mimics - Differential Diagnosis Framework
Diffuse alveolar hemorrhage + rapidly progressive glomerulonephritis
90%:
 -
Pulmonary Renal ... - Differential Diagnosis ... Complement Levels: SLE, Cryoglobulinemic ... Levels: Scleroderma Renal ... #Differential #Diagnosis
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
- Differential Diagnosis ... POEMS, AL amyloid, Cryoglobulinemia ... Schnitzler syndrome • Cryoglobulinemia ... Renal-centered ... #Differential #Diagnosis
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... (Pulmonary and renal ... Differential Diagnosis ... Behcet disease, Cryoglobulinemia ... #differential #diagnosis
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Mnemonic C - Cryoglobulinemia ... Erythematosus (total 50, renal ... CHAMPS #Mnemonic #diagnosis
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Immunotactoid GN & Cryoglobulinemic ... WM: Vasculitis (Cryoglobulinemic ... vascular beds-renal ... #Differential #Diagnosis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... pulmonary and renal ... ANCA +MPO) • Cryoglobulinemic ... Low levels mixed cryoglobulinemia ... • Urinalysis (Renal
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Non-hepatitis C virus Cryoglobulinemia ... MONOCLONAL CRYOGLOBULINEMIA ... lenalinomide MIXED CRYOGLOBULINEMIA ... TerrierBen #NonHCV #Cryoglobulinemia ... Monoclonal #Mixed #Cryoglobulinemic