95 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Vasculitis - French ... Vasculitis Study ... Target plasma cells ... #Vasculitis #Management ... #Rheumatology #
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Vasculitis 1 ... not related to clinical ... 3 types 2) Vasculitis ... Hyperviscosity syndrome ... #Rheumatology #
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
, causes and management ... - French Vasculitis ... vasculitis Clinical ... #Vasculitis #Rheumatology ... #Diagnosis #Management
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
in 35% of mixed cryoglobulinemia ... vasculitis Associated ... #Vasculitis #Management ... #Rheumatology # ... Cryoglobulinemic
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Hyperviscosity Syndrome ... Syndrome: • Clinical ... syndrome in 80% ... 20% Sjögren's syndrome ... classification #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... Urticarial/LCV) - Cryoglobulinemic ... Disease • Cogan syndrome ... #skin #dermatology ... #rheumatology #
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
deposits: Type I cryoglobulinemia ... activity: Type II cryoglobulinemia ... , Syndrome Schnitzler ... manifestations #dermatology ... #skin #clinical
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
semiology of Cutaneous Vasculitis ... hemopathies (4%) • Cryoglobulinemia ... vasculitis (3%) ... #dermpath #dermatology ... lesions #diagnosis #clinical
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Rarely dominate the clinical ... Maculopapular rash ... purpura • Mixed cryoglobulinemia ... • Goodpasture syndrome ... #rash #diagnosis
Fever and Rash - Differential Diagnosis Framework
 • Viral: Measles, Infectious Mono (EBV, CMV), Acute HIV,
Fever and Rash - ... diseases, Toxic shock syndrome ... , DRESS, Sweet syndrome ... , Vasculitis SCVMC ... SCVMCMed #Fever #Rash