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Cutaneous Lupus Erythematosus
Acute - Subacute - Chronic - Intermittent

- Dr. Florence Delestre

#Cutaneous #Lupus #Erythematosus #SLE #rheumatology
Cutaneous Lupus ... Florence Delestre #Cutaneous ... Erythematosus #SLE
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Dermatological semiology of Cutaneous ... the context of cutaneous ... vasculitis • Cutaneous ... disease (10%) : SLE ... TerrierBen #Cutaneous
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Primary: 50% Cutaneous ... Secondary: CTD: SLE ... EGPA - GPA Cutaneous ... Vasculitis: • Cutaneous ... Cogan syndrome #Cutaneous
SLICC SLE Diagnostic Criteria - Systemic Lupus Erythematosus
Clinical and Immunologic Criteria

CLINICAL CRITERIA
 - ACUTE CUTANEOUS LUPUS
SLICC SLE Diagnostic ... CRITERIA - ACUTE CUTANEOUS ... LUPUS OR SUBACUTE CUTANEOUS ... LUPUS - CHRONIC CUTANEOUS ... #Rheumatology #SLE
Cutaneous manifestations associated with myelodysplastic syndrome
 • Myeloid hemopathy with the most frequent skin lesions (20%)
Cutaneous manifestations ... dermatomyositis, SLE ... Calmettes #Cutaneous
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
Induced Lupus vs SLE ... Rare (SSA+ for cutaneous ... rare), Topics for cutaneous-DIL ... Erythematosus (SLE ... management of SLE
EULAR/ACR Classification Criteria for Systemic Lupus Erythematosus
Clinical Domains:
 • Constitutional domain: Fever
 • Cutaneous domain: Non-scarring
domain: Fever • Cutaneous ... ulcers, Subacute cutaneous ... discoid lupus, Acute cutaneous ... Classification #Criteria #SLE
Systemic Lupus Erythematosus - Diagnosis
Manifestations:
 - Arthritis 69%
 - Malar rash 40%
 - Fever 36%
 -
involvement 3% SLE-Related ... Drug-induced lupus, Cutaneous ... Lupusreference #SLE
Lupus (SLE): Mucocutaneous Manifestations

 • Langerhan cells and keratinocytes release cytokines -> localized inflammatory response ->
Lupus (SLE): Mucocutaneous ... response -> Subacute cutaneous ... Phenomenon #Lupus #SLE
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Classification: • Acute cutaneous ... scarring • Subacute cutaneous ... inflammation Cutaneous ... : Drug induced SLE ... SSA can rule in SLE