137 results
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
: • Primary amyloid ... Bone/Joint: • Amyloid ... (AMYLOID ANGIOPATHY ... Protein • AL Amyloid ... #Diagnosis #Amyloid
Amyloidosis Diagnosis
1) Patient presentation
 • Cardiac-specific signs of amyloidosis: Diastolic heart failure, Heart failure with preserved
Amyloidosis Diagnosis ... Cardiac-specific signs of amyloidosis ... Noncardiac signs of amyloidosis ... 2) Methods of amyloid ... chain levels 3) Amyloid
Amyloidosis - Workup and Diagnostic Algorithm
 • Serum Immunofixation and Serum Free Light Chains
 • Biopsy
Amyloidosis - Workup ... tests after AL amyloidosis ... Confirm type of amyloid ... TnT, proBNP #Amyloidosis
Cardiac Amyloidosis Management
The liver produces transthyretin tetramers, which dissociate into monomers and mis-fold, then aggregate into
Cardiac Amyloidosis ... aggregate into amyloid ... Cardiac amyloidosis ... yeeann_c #Cardiac #Amyloidosis
Cardiac Amyloid - Diagnosis, Signs, Symptoms and Management

Clinical Presentation
- exertional dyspnea
- peripheral edema
- exertional syncope
- peripheral
Cardiac Amyloid ... cardionerds #Amyloidosis
Etiologies of Peripheral Neuropathy
 • Metabolic / Nutritional: DiabetesB12 deficiency, Uremia/ESRD, Hypothyroidism
 • Medication-induced: ART, Antibiotics,
, Sarcoidosis, Amyloidosis ... myeloma, secondary amyloid
Restrictive Cardiomyopathy - Diagnosis and Causes
Clinical: Dyspnea, Exercise Intolerance, ↑ "Right Sided-Symptoms" (ascites, hepatomegaly, ↑↑peripheral edema)
Physical
Infiltrative: Amyloidosis ... (AL Amyloid, Wild
Ankylosing Spondylitis: Extra-articular Manifestations
 • Ocular - Inflammation of the iris, the anterior part of the
including serum amyloid ... Deposition of amyloid ... glomeruli -> Secondary Amyloidosis
Therapy for AL Amyloidosis 2019 
 - Antibodies (Plasma cells) 
 - Proteasome Inhibitors 
 -
Therapy for AL Amyloidosis ... Amyloid_Planet #Amyloidosis ... #ALAmyloidosis
Amyloidosis Types - Comparison Table
Proteins depositing where they shouldn't
 • AL
 • TTR
 • AA

Julia Gips,
Amyloidosis Types ... juliagips15 #Amyloidosis