1890 results
Pathophysiology of Hemolytic Anemia
 - Defects in RBC internal contents (thalassemia, hemoglobinopathies, and metabolic defects)
 -
Hemolytic Anemia - Defects ... and metabolic defects ... ) - Defects in ... rnembranes - Defects ... Hemolytic #Anemia #hematology
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... Bernard-Soulier Syndrome • Defect ... Thrombasthenia • Defect ... Related Disorder • Defect ... differential #diagnosis #hematology
Hemolytic Anemias - Differential Diagnosis Algorithm

Signs of anemia and hemolysis:
 • ↓ Haptoglobin
 • ↑ LDH
Extrinsic RBC Defects ... Intrinsic RBC Defects ... : Membrane defects ... Diagnosis #Algorithm #hematology
Causes of Bleeding / Bruising - Differential Diagnosis Algorithm
Thrombocytopenia - Quantitative Defect
 • Decreased Production
 •
- Quantitative Defect ... - Qualitative Defect ... Algorithm #Causes #Hematology
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
Non-immune: Membrane Defects ... Spiders - Enzyme Defects ... - Hemoglobin Defects ... Differential #Diagnosis #hematology
Causes of Extravascular and Intravascular Hemolysis - Differential Diagnosis Algorithm
Extravascular - Spleen and RES-mediated hemolysis
 -
Abnormal Hgb & Hgb Defects ... Hgb - Membrane Defects ... - RBC Enzyme Defects ... Algorithm #Causes #Hematology
Von Willebrand Disease Classification
Type 1 (Accounts for ~3/4 of cases):
 • Defect: Quantitative defect (i.e. not
of cases): • Defect ... : Quantitative defect ... , 2M, 2N): • Defect ... : Qualitative defect ... Types #diagnosis #hematology
Hemolytic Anemia - Differential Diagnosis Algorithm
 • Sickle cells - Consider sickle cell disease (diverse genotypes):
, Other enzyme defects ... Unstable hemoglobin defects ... Glutathione metabolism defects ... Algorithm #workup #hematology
Thrombocytopenia and Pregnancy
Three syndromes in the critically ill pregnant woman who presents with coagulation defects.
1) HELLP
with coagulation defects ... Severe coagulation defects ... Obstetrics #OBGyn #Hematology
Thrombocytopenia and Pregnancy - TTP/HUS, HELLP Syndrome and Acute Fatty Liver of Pregnancy (AFLP)
Three syndromes in
with coagulation defects ... Severe coagulation defects ... AFLP #obstetrics #hematology