15 results
Systemic Sclerosis (Scleroderma)
Multi-system autoimmune disease characterized by vasculopathy and progressive fibrosis of skin and internal organs
3
autoimmune disease ... and progressive fibrosis ... : ILD (interstitial ... lung disease), ... Scleroderma #SSc #rheumatology
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
- Summary Antinuclear ... Treatment: • ... Mild disease- Hydroxychloroquine ... Erythematosus #SLE #Summary ... #diagnosis #rheumatology
Management of interstitial lung disease (ILD)-associated with systemic sclerosis (SSc)

Therapeutic indication: absolute decline in FVC >10%
interstitial lung disease ... (ILD)-associated ... with systemic sclerosis ... systemicsclerosis #SSc #pulmonary ... #algorithm
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
solid cancers • Systemic ... mevalonate kinase deficiency ... hepatitis • Pulmonary ... diagnosis #management #treatment ... #rheumatology
Approach to Thrombocytosis - Elevated Platelet Count - Differential Diagnosis Algorithm

Peripheral Smear concerning for malignancy?
Differential Diagnosis Algorithm ... Acute hemolysis, deficiency ... Rebound effect from treatment ... Inflammatory Conditions: Rheumatologic ... , Celiac disease
Iron Deficiency Anemia - Differential Diagnosis Algorithm

Labs: Ferritin, iron, transferrin, TIBC, TSAT, sTfR

 • Blood loss:
Differential Diagnosis Algorithm ... athletic training, Pulmonary ... Structural: Celiac disease ... Tropical sprue, IBD ... #ferritin #hematology
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
Inflammatory: • IBD ... disorders • Celiac disease ... effect following treatment ... malignancy • Iron deficiency ... #Causes #Hematology
Causes of Interstitial Lung Disease - Differential Diagnosis Algorithm
Idiopathic Interstitial Pneumonia
 • (UIP) Usual Interstitial Pneumonia
Differential Diagnosis Algorithm ... Interstitial Pneumonia - fibrosis ... leaking out of pulmonary ... Rheumatoid Arthritis, Systemic ... #ILD #Causes #Differential
Short Stature - Differential Diagnosis Algorithm
Normal Variant, Normal Puberty Onset (BA = CA)
 • Familial Short
Differential Diagnosis Algorithm ... • GH Deficiency ... Panhypopituitarism Treatment ... Celiac, IBD) • ... Cystic Fibrosis,
Hemophagocytic Lymphohistiocytosis (HLH)
Pathophysiology: Triggering factor (infection,...)→Activation of CD8 T cells (IFN-y) → Excessive activation of macrophages
cytokines (TNFa,lL1, IL6 ... • Autoimmune diseases ... Cellular immune deficiency ... Unknown cause Treatment ... #summary #rheumatology